Gene Directory

621 genes with known genetic variants in our database.

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All Chr 1(621) Chr 2(446) Chr 3(370) Chr 4(242) Chr 5(266) Chr 6(311) Chr 7(286) Chr 8(216) Chr 9(250) Chr 10(250) Chr 11(386) Chr 12(324) Chr 13(111) Chr 14(198) Chr 15(221) Chr 16(276) Chr 17(359) Chr 18(87) Chr 19(346) Chr 20(177) Chr 21(71) Chr 22(147) Chr X(397) Chr Y(4)
USH2A
usherin
2089 variants Chr 1 "Fibronectin type III domain c...
ABCA4
ATP binding cassette subfamily A member 4
1388 variants Chr 1 "ATP binding cassette subfamil...
MUTYH
mutY DNA glycosylase
862 variants Chr 1 DNA glycosylases
RYR2
ryanodine receptor 2
853 variants Chr 1 "Ryanodine receptors|EF-hand d...
LMNA
lamin A/C
613 variants Chr 1 Lamins
AGL
amylo-alpha-1,6-glucosidase and 4-alpha-glucanotransferase
570 variants Chr 1 Glycoside hydrolase family
CRB1
crumbs cell polarity complex component 1
556 variants Chr 1 Crumbs complex components
FH
fumarate hydratase
544 variants Chr 1
ASPM
assembly factor for spindle microtubules
458 variants Chr 1
COL11A1
collagen type XI alpha 1 chain
452 variants Chr 1 Fibrillar collagens
CACNA1S
calcium voltage-gated channel subunit alpha1 S
450 variants Chr 1 Calcium voltage-gated channel ...
ALPL
alkaline phosphatase, biomineralization associated
420 variants Chr 1 Alkaline phosphatases
SPTA1
spectrin alpha, erythrocytic 1
348 variants Chr 1 "EF-hand domain containing|Spe...
SLC2A1
solute carrier family 2 member 1
346 variants Chr 1 Solute carrier family 2
LYST
lysosomal trafficking regulator
340 variants Chr 1 "WD repeat domain containing|B...
ACADM
acyl-CoA dehydrogenase medium chain
326 variants Chr 1 "Acyl-CoA dehydrogenase family...
LAMB3
laminin subunit beta 3
315 variants Chr 1 "Laminin subunits|MicroRNA pro...
HSPG2
heparan sulfate proteoglycan 2
312 variants Chr 1 "Proteoglycans|I-set domain co...
POMGNT1
protein O-linked mannose N-acetylglucosaminyltransferase 1 (beta 1,2-)
303 variants Chr 1 O-linked N-acetylglucosaminylt...
SDHB
succinate dehydrogenase complex iron sulfur subunit B
283 variants Chr 1 Mitochondrial complex II: succ...
NPHP4
nephrocystin 4
274 variants Chr 1 NPHP complex
RPE65
retinoid isomerohydrolase RPE65
258 variants Chr 1
CPT2
carnitine palmitoyltransferase 2
249 variants Chr 1 Carnitine palmitoyltransferase...
LAMC2
laminin subunit gamma 2
235 variants Chr 1 Laminin subunits
NTRK1
neurotrophic receptor tyrosine kinase 1
232 variants Chr 1 "Receptor tyrosine kinases|Imm...
MFN2
mitofusin 2
229 variants Chr 1 Mitofusin family
ARID1A
AT-rich interaction domain 1A
224 variants Chr 1 "AT-rich interaction domain co...
SZT2
SZT2 subunit of KICSTOR complex
223 variants Chr 1 "KICSTOR complex|MicroRNA prot...
AHDC1
AT-hook DNA binding motif containing 1
222 variants Chr 1
ACTN2
actinin alpha 2
219 variants Chr 1 Actinins
FLG
filaggrin
211 variants Chr 1 "EF-hand domain containing|S10...
NOTCH2
notch receptor 2
210 variants Chr 1 Notch receptors
POGZ
pogo transposable element derived with ZNF domain
206 variants Chr 1 "Zinc fingers C2H2-type|Helix-...
MPZ
myelin protein zero
202 variants Chr 1 "V-set domain containing|Ig-li...
MTHFR
methylenetetrahydrofolate reductase
202 variants Chr 1 Flavoproteins
ACTA1
actin alpha 1, skeletal muscle
197 variants Chr 1 Actins
ATP1A2
ATPase Na+/K+ transporting subunit alpha 2
187 variants Chr 1 ATPase Na+/K+ transporting sub...
GBA1
glucosylceramidase beta 1
180 variants Chr 1 "Glycoside hydrolase family|Gl...
MPL
MPL proto-oncogene, thrombopoietin receptor
179 variants Chr 1 "CD molecules|Fibronectin type...
CDC73
cell division cycle 73
176 variants Chr 1 "Paf1/RNA polymerase II comple...
DPYD
dihydropyrimidine dehydrogenase
174 variants Chr 1 Flavoproteins
HNRNPU
heterogeneous nuclear ribonucleoprotein U
173 variants Chr 1 Heterogeneous nuclear ribonucl...
ADAMTSL4
ADAMTS like 4
172 variants Chr 1 "ADAMTS like|MicroRNA protein ...
ATP13A2
ATPase cation transporting 13A2
172 variants Chr 1 ATPase orphan transporters
MMACHC
metabolism of cobalamin associated C
167 variants Chr 1 Flavoproteins
PCSK9
proprotein convertase subtilisin/kexin type 9
167 variants Chr 1 Proprotein convertase subtilis...
PPT1
palmitoyl-protein thioesterase 1
167 variants Chr 1 Depalmitoylases
F5
coagulation factor V
163 variants Chr 1 Multicopper oxidase family
DBT
dihydrolipoamide branched chain transacylase E2
162 variants Chr 1 Branched chain alpha-keto acid...
P3H1
prolyl 3-hydroxylase 1
159 variants Chr 1 Prolyl 3-hydroxylase family
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