LPL Chromosome 8

Lipoprotein lipase
147 variants 147 Health Risk

Upload your DNA to see your personal genotypes for variants in LPL.

What This Gene Does
LPL encodes lipoprotein lipase, which is expressed in heart, muscle, and adipose tissue. LPL functions as a homodimer, and has the dual functions of triglyceride hydrolase and ligand/bridging factor for receptor-mediated lipoprotein uptake. Severe mutations that cause LPL deficiency result in type I hyperlipoproteinemia, while less extreme mutations in LPL are linked to many disorders of lipoprotein metabolism. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Lipases
Locus Type
gene with protein product
Location
8p21.3
Ensembl
ENSG00000175445
Associated Conditions (13)
Hyperlipoproteinemia
type I
Cardiovascular phenotype
LPL-related disorder
Hyperlipidemia
familial combined
LPL related
Hypertriglyceridemia
susceptibility to
Dilated cardiomyopathy 1A
LIPOPROTEIN LIPASE (OLBIA)
Lipase deficiency
combined
Key Variants
All Variants (147)
RSID Category Clinical Significance Conditions
RS114726797 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS116403115 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS1297688787 Health Risk Conflicting classifications of pathogenicity Hypertriglyceridemia, Hyperlipoproteinemia, type I
RS1389582732 Health Risk Conflicting classifications of pathogenicity Hyperlipidemia, familial combined, LPL related
RS140457997 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS140986245 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS1425981651 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS144466625 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipidemia
RS147309575 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS150319057 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipidemia
RS1800011 Health Risk Conflicting classifications of pathogenicity Hyperlipidemia, familial combined, LPL related
RS199606532 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS201946950 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS2070033114 Health Risk Conflicting classifications of pathogenicity Hyperlipidemia, familial combined, LPL related
RS2128838568 Health Risk Conflicting classifications of pathogenicity
RS2540107214 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Hyperlipidemia, familial combined
RS268 Health Risk Conflicting classifications of pathogenicity Hyperlipidemia, familial combined, LPL related
RS298 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Cardiovascular phenotype
RS45607438 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS527267420 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Cardiovascular phenotype
RS540525285 Health Risk Conflicting classifications of pathogenicity LPL-related disorder, LPL-related disorder
RS557015233 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Dilated cardiomyopathy 1A
RS747055420 Health Risk Conflicting classifications of pathogenicity
RS749390229 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS758248912 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS762007406 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipidemia
RS764871141 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS76708715 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS776585907 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS886037775 Health Risk Conflicting classifications of pathogenicity Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS1064797075 Health Risk Likely pathogenic Hyperlipidemia, familial combined, LPL related
RS1157393817 Health Risk Likely pathogenic
RS118204056 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS118204061 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipidemia
RS118204076 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS118204077 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Cardiovascular phenotype
RS118204078 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS1409123950 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipidemia
RS1554517725 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS2069980707 Health Risk Likely pathogenic
RS2070032216 Health Risk Likely pathogenic Hyperlipoproteinemia, type I, Hyperlipoproteinemia
RS2128836980 Health Risk Likely pathogenic
RS2128838006 Health Risk Likely pathogenic
RS2128838178 Health Risk Likely pathogenic
RS2128839227 Health Risk Likely pathogenic Hyperlipidemia, familial combined, LPL related
RS2128839623 Health Risk Likely pathogenic
RS2128839831 Health Risk Likely pathogenic
RS2540092140 Health Risk Likely pathogenic
RS2540092337 Health Risk Likely pathogenic
RS2540103100 Health Risk Likely pathogenic
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