TP53 Chromosome 17

Tumor protein p53
1152 variants 1 Drug Response 1151 Health Risk

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What This Gene Does
This gene encodes a tumor suppressor protein containing transcriptional activation, DNA binding, and oligomerization domains. The encoded protein responds to diverse cellular stresses to regulate expression of target genes, thereby inducing cell cycle arrest, apoptosis, senescence, DNA repair, or changes in metabolism. Mutations in this gene are associated with a variety of human cancers, including hereditary cancers such as Li-Fraumeni syndrome. Alternative splicing of this gene and the use of alternate promoters result in multiple transcript variants and isoforms. Additional isoforms have also been shown to result from the use of alternate translation initiation codons from identical transcript variants (PMIDs: 12032546, 20937277). [provided by RefSeq, Dec 2016]
Associated Conditions (136)
Poly (ADP-Ribose) polymerase inhibitor response
Li-Fraumeni syndrome
Hereditary cancer-predisposing syndrome
Li-Fraumeni syndrome 1
Familial cancer of breast
Squamous cell carcinoma of the head and neck
Adrenocortical carcinoma
hereditary
Breast and/or ovarian cancer
Diffuse glioma
H3 G34 mutant
Colorectal cancer
Malignant tumor of esophagus
Neoplasm
Astrocytoma IDH-mutant
Ovarian neoplasm
Embryonal rhabdomyosarcoma
Lung cancer
Choroid plexus carcinoma
TP53-related disorder
+116 more conditions
Key Variants
RS1057519625
drug response
Poly (ADP-Ribose) polymerase inhibitor response, Poly (ADP-Ribose) polymerase inhibitor response
Drug Response
RS1008479744
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
Health Risk
RS1042522
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
Health Risk
RS1044102603
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome 1, Li-Fraumeni syndrome 1
Health Risk
RS1046611742
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
Health Risk
RS1048095040
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Familial cancer of breast
Health Risk
RS1057517593
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome 1, Li-Fraumeni syndrome, Breast and/or ovarian cancer
Health Risk
RS1057519747
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Adrenocortical carcinoma, hereditary
Health Risk
RS1057519976
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
Health Risk
RS1057519978
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
Health Risk
RS1057519981
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
Health Risk
RS1057519982
Conflicting classifications of pathogenicity
Li-Fraumeni syndrome 1, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
Health Risk
All Variants (1152)
RSID Category Clinical Significance Conditions
RS1057519625 Drug Response drug response Poly (ADP-Ribose) polymerase inhibitor response, Poly (ADP-Ribose) polymerase inhibitor response
RS1008479744 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1042522 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1044102603 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome 1, Li-Fraumeni syndrome 1
RS1046611742 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1048095040 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Familial cancer of breast
RS1057517593 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome 1, Li-Fraumeni syndrome, Breast and/or ovarian cancer
RS1057519747 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Adrenocortical carcinoma, hereditary
RS1057519976 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1057519978 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1057519981 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1057519982 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome 1, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1057519983 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1057519986 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Li-Fraumeni syndrome 1, Hereditary cancer-predisposing syndrome
RS1057519987 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1057519988 Health Risk Conflicting classifications of pathogenicity Ovarian neoplasm, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1057519991 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Ovarian neoplasm, Hereditary cancer-predisposing syndrome
RS1057519995 Health Risk Conflicting classifications of pathogenicity Ovarian neoplasm, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1057519996 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Ovarian neoplasm, Hereditary cancer-predisposing syndrome
RS1057519998 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Ovarian neoplasm
RS1057519999 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1057520001 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Ovarian neoplasm, Li-Fraumeni syndrome 1
RS1057520003 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1057520004 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Neoplasm
RS1057520005 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Lip and oral cavity carcinoma, Hereditary cancer-predisposing syndrome
RS1057520006 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Hereditary cancer-predisposing syndrome
RS1057520607 Health Risk Conflicting classifications of pathogenicity Ovarian neoplasm, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1057521167 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1057522275 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Adrenocortical carcinoma
RS1057522496 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1060501190 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1060501198 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1060501199 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1060501201 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Bone osteosarcoma, Li-Fraumeni syndrome 1
RS1060501202 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1060501203 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome
RS1060501208 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1060501211 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1060504160 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1060504161 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Li-Fraumeni syndrome 1, Li-Fraumeni syndrome
RS1060504163 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Li-Fraumeni syndrome 1, Li-Fraumeni syndrome
RS1064793603 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
RS1064793810 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Li-Fraumeni syndrome 1, Hereditary cancer-predisposing syndrome
RS1064793881 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Squamous cell carcinoma of the head and neck, Ovarian neoplasm
RS1064794312 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1064794810 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1064795056 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome 1
RS1064795139 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome 1, Li-Fraumeni syndrome, Hereditary cancer-predisposing syndrome
RS1064795691 Health Risk Conflicting classifications of pathogenicity Li-Fraumeni syndrome, Li-Fraumeni syndrome 1, Hereditary cancer-predisposing syndrome
RS1064795860 Health Risk Conflicting classifications of pathogenicity Hereditary cancer-predisposing syndrome, Li-Fraumeni syndrome, Li-Fraumeni syndrome 1
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