MERTK Chromosome 2

MER proto-oncogene, tyrosine kinase
139 variants 139 Health Risk

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What This Gene Does
This gene is a member of the MER/AXL/TYRO3 receptor kinase family and encodes a transmembrane protein with two fibronectin type-III domains, two Ig-like C2-type (immunoglobulin-like) domains, and one tyrosine kinase domain. Mutations in this gene have been associated with disruption of the retinal pigment epithelium (RPE) phagocytosis pathway and onset of autosomal recessive retinitis pigmentosa (RP). [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"Receptor tyrosine kinases|Fibronectin type III domain containing|I-set domain containing"
Locus Type
gene with protein product
Location
2q13
Ensembl
ENSG00000153208
Associated Conditions (27)
Retinal dystrophy
Retinitis pigmentosa
Retinitis pigmentosa 38
MERTK-related disorder
Inborn genetic diseases
Optic atrophy
Familial pancreatic carcinoma
Lymphoma
Adrenocortical carcinoma
hereditary
Ovarian cancer
Chronic lymphocytic leukemia/small lymphocytic lymphoma
Sarcoma
Nonpapillary renal cell carcinoma
Cervical cancer
Uterine carcinosarcoma
Thymoma
Thyroid cancer
nonmedullary
1
+7 more conditions
Key Variants
All Variants (139)
RSID Category Clinical Significance Conditions
RS112257146 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS112541306 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS113485015 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1265437249 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS1309440527 Health Risk Conflicting classifications of pathogenicity
RS1323896467 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1342715176 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS138908058 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, MERTK-related disorder, Retinitis pigmentosa
RS141361084 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 38, Retinal dystrophy, Retinal dystrophy
RS141647333 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, MERTK-related disorder, Inborn genetic diseases
RS142985827 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa
RS144751432 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Optic atrophy, Retinitis pigmentosa
RS147899488 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinitis pigmentosa 38, Retinal dystrophy
RS149131360 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS1553452169 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1558793454 Health Risk Conflicting classifications of pathogenicity
RS1677512620 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1681147109 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS200363872 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS2230516 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 38, Retinitis pigmentosa, MERTK-related disorder
RS34072093 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa
RS34943572 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa 38
RS35252762 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS35898499 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa 38, Familial pancreatic carcinoma
RS373198570 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, MERTK-related disorder, Retinitis pigmentosa
RS3761702 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, MERTK-related disorder
RS527236084 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 38, Retinitis pigmentosa, Retinitis pigmentosa 38
RS527694612 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, MERTK-related disorder, Retinitis pigmentosa
RS541717028 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa 38
RS557004700 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS55924349 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa 38, Retinitis pigmentosa
RS56225811 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS745461381 Health Risk Conflicting classifications of pathogenicity Retinal disorder, Retinal disorder
RS747835003 Health Risk Conflicting classifications of pathogenicity
RS747894786 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS749472520 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS752112582 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS757858711 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Inborn genetic diseases, Retinal dystrophy
RS772204397 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinitis pigmentosa 38, Retinal dystrophy
RS772574056 Health Risk Conflicting classifications of pathogenicity MERTK-related disorder, MERTK-related disorder
RS79943145 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa
RS886054757 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1252719064 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS142721656 Health Risk Likely pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1553454799 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1553458060 Health Risk Likely pathogenic
RS1573592033 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1573592124 Health Risk Likely pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1573607809 Health Risk Likely pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1573627154 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
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