MERTK Chromosome 2

MER proto-oncogene, tyrosine kinase
139 variants 139 Health Risk

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What This Gene Does
This gene is a member of the MER/AXL/TYRO3 receptor kinase family and encodes a transmembrane protein with two fibronectin type-III domains, two Ig-like C2-type (immunoglobulin-like) domains, and one tyrosine kinase domain. Mutations in this gene have been associated with disruption of the retinal pigment epithelium (RPE) phagocytosis pathway and onset of autosomal recessive retinitis pigmentosa (RP). [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"Receptor tyrosine kinases|Fibronectin type III domain containing|I-set domain containing"
Locus Type
gene with protein product
Location
2q13
Ensembl
ENSG00000153208
Associated Conditions (27)
Retinal dystrophy
Retinitis pigmentosa
Retinitis pigmentosa 38
MERTK-related disorder
Inborn genetic diseases
Optic atrophy
Familial pancreatic carcinoma
Lymphoma
Adrenocortical carcinoma
hereditary
Ovarian cancer
Chronic lymphocytic leukemia/small lymphocytic lymphoma
Sarcoma
Nonpapillary renal cell carcinoma
Cervical cancer
Uterine carcinosarcoma
Thymoma
Thyroid cancer
nonmedullary
1
+7 more conditions
Key Variants
All Variants (139)
RSID Category Clinical Significance Conditions
RS1573648098 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1676864249 Health Risk Likely pathogenic
RS1676864420 Health Risk Likely pathogenic
RS1676864515 Health Risk Likely pathogenic
RS1677289241 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1684627892 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1684937955 Health Risk Likely pathogenic
RS1684979540 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1685339034 Health Risk Likely pathogenic
RS2104406867 Health Risk Likely pathogenic
RS2104406873 Health Risk Likely pathogenic
RS2104413016 Health Risk Likely pathogenic
RS2104652801 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS527236134 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS761251269 Health Risk Likely pathogenic
RS778005207 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS778383770 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS786205535 Health Risk Likely pathogenic Autosomal recessive retinitis pigmentosa, Retinitis pigmentosa 38, Autosomal recessive retinitis pigmentosa
RS863224894 Health Risk Likely pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS878853355 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1187387547 Health Risk Pathogenic Retinal dystrophy, Retinal dystrophy
RS119489105 Health Risk Pathogenic Retinitis pigmentosa 38, Autosomal recessive retinitis pigmentosa, Retinitis pigmentosa
RS1243173716 Health Risk Pathogenic
RS1309140887 Health Risk Pathogenic Retinitis pigmentosa 38, Retinal dystrophy, Retinitis pigmentosa 38
RS1337364058 Health Risk Pathogenic
RS1371550108 Health Risk Pathogenic
RS1400057476 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1487540503 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1553449458 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1573554264 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1573638426 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1676689811 Health Risk Pathogenic Autosomal recessive retinitis pigmentosa, Retinitis pigmentosa 38, Autosomal recessive retinitis pigmentosa
RS1676862579 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1676864299 Health Risk Pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1676904823 Health Risk Pathogenic Retinal dystrophy, Retinal disorder, Retinal dystrophy
RS1676926630 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS1677065097 Health Risk Pathogenic Autosomal recessive retinitis pigmentosa, Autosomal recessive retinitis pigmentosa
RS1677347565 Health Risk Pathogenic
RS1677368092 Health Risk Pathogenic
RS1677514061 Health Risk Pathogenic
RS2104407571 Health Risk Pathogenic
RS2104411620 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS2104421764 Health Risk Pathogenic
RS2104423657 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS2104423659 Health Risk Pathogenic Retinitis pigmentosa 38, Retinitis pigmentosa 38
RS2104424446 Health Risk Pathogenic
RS2104686582 Health Risk Pathogenic
RS2104733931 Health Risk Pathogenic
RS2104741154 Health Risk Pathogenic
RS2466693520 Health Risk Pathogenic
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