LAMP2 Chromosome X

Lysosome associated membrane protein 2
169 variants 169 Health Risk

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What This Gene Does
The protein encoded by this gene is a member of a family of membrane glycoproteins. This glycoprotein provides selectins with carbohydrate ligands. It may play a role in tumor cell metastasis. It may also function in the protection, maintenance, and adhesion of the lysosome. Alternative splicing of this gene results in multiple transcript variants encoding distinct proteins. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"CD molecules|Lysosome associated membrane proteins"
Locus Type
gene with protein product
Location
Xq24
Ensembl
ENSG00000005893
Associated Conditions (16)
Danon disease
Cardiovascular phenotype
Cardiomyopathy
Hypertrophic cardiomyopathy
Intellectual disability
LAMP2-related disorder
Nonpapillary renal cell carcinoma
Primary dilated cardiomyopathy
Trifascicular block on electrocardiogram
Primary familial hypertrophic cardiomyopathy
Melanoma
Thyroid cancer
nonmedullary
1
Malignant tumor of urinary bladder
Isolated Noncompaction of the Ventricular Myocardium
Key Variants
All Variants (169)
RSID Category Clinical Significance Conditions
RS1921041608 Health Risk Pathogenic
RS1921053197 Health Risk Pathogenic Danon disease, Danon disease
RS1921109201 Health Risk Pathogenic Danon disease, Danon disease
RS1921663802 Health Risk Pathogenic Danon disease, Danon disease
RS2058573264 Health Risk Pathogenic Danon disease, Danon disease
RS2058596487 Health Risk Pathogenic Danon disease, Danon disease
RS2058605108 Health Risk Pathogenic Danon disease, Danon disease
RS2058610123 Health Risk Pathogenic
RS2147278850 Health Risk Pathogenic Danon disease, Danon disease
RS2147278864 Health Risk Pathogenic Danon disease, Danon disease
RS2147278957 Health Risk Pathogenic Danon disease, Danon disease
RS2147281356 Health Risk Pathogenic Danon disease, Danon disease
RS2147282355 Health Risk Pathogenic Danon disease, Danon disease
RS2147282415 Health Risk Pathogenic Isolated Noncompaction of the Ventricular Myocardium, Isolated Noncompaction of the Ventricular Myocardium
RS2147282434 Health Risk Pathogenic Danon disease, Thyroid cancer, nonmedullary
RS2147283096 Health Risk Pathogenic Danon disease, Danon disease
RS2147286730 Health Risk Pathogenic Danon disease, Danon disease
RS2147287565 Health Risk Pathogenic Danon disease, Danon disease
RS2147287579 Health Risk Pathogenic
RS2147287624 Health Risk Pathogenic Primary dilated cardiomyopathy, Danon disease, Primary dilated cardiomyopathy
RS2147287637 Health Risk Pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS2147287645 Health Risk Pathogenic Danon disease, Danon disease
RS2147287657 Health Risk Pathogenic Cardiomyopathy, Cardiomyopathy
RS2147294800 Health Risk Pathogenic Danon disease, Danon disease
RS2147294814 Health Risk Pathogenic Danon disease, Danon disease
RS2520860264 Health Risk Pathogenic Danon disease, Danon disease
RS2520864428 Health Risk Pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS2520877178 Health Risk Pathogenic Danon disease, Danon disease
RS2520877438 Health Risk Pathogenic Danon disease, Danon disease
RS2520884260 Health Risk Pathogenic Danon disease, Danon disease
RS2520884782 Health Risk Pathogenic Danon disease, Danon disease
RS2520884993 Health Risk Pathogenic Danon disease, Danon disease
RS2520906991 Health Risk Pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS2520907960 Health Risk Pathogenic Danon disease, Danon disease
RS2520908238 Health Risk Pathogenic Danon disease, Danon disease
RS2520908416 Health Risk Pathogenic Danon disease, Danon disease
RS2520912970 Health Risk Pathogenic Danon disease, Danon disease
RS2520913146 Health Risk Pathogenic Danon disease, Danon disease
RS2520913315 Health Risk Pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS2520913421 Health Risk Pathogenic Danon disease, Danon disease
RS2520913492 Health Risk Pathogenic Danon disease, Danon disease
RS2520913626 Health Risk Pathogenic Danon disease, Danon disease
RS397516738 Health Risk Pathogenic Hypertrophic cardiomyopathy, Danon disease, Hypertrophic cardiomyopathy
RS397516740 Health Risk Pathogenic Danon disease, Nonpapillary renal cell carcinoma, Danon disease
RS397516743 Health Risk Pathogenic Danon disease, Danon disease
RS398123685 Health Risk Pathogenic
RS727503118 Health Risk Pathogenic Danon disease, Hypertrophic cardiomyopathy, Cardiovascular phenotype
RS727503119 Health Risk Pathogenic Danon disease, Thyroid cancer, nonmedullary
RS727504597 Health Risk Pathogenic Primary dilated cardiomyopathy, Danon disease, Primary dilated cardiomyopathy
RS727504600 Health Risk Pathogenic Danon disease, Danon disease
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