LAMP2 Chromosome X

Lysosome associated membrane protein 2
169 variants 169 Health Risk

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What This Gene Does
The protein encoded by this gene is a member of a family of membrane glycoproteins. This glycoprotein provides selectins with carbohydrate ligands. It may play a role in tumor cell metastasis. It may also function in the protection, maintenance, and adhesion of the lysosome. Alternative splicing of this gene results in multiple transcript variants encoding distinct proteins. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"CD molecules|Lysosome associated membrane proteins"
Locus Type
gene with protein product
Location
Xq24
Ensembl
ENSG00000005893
Associated Conditions (16)
Danon disease
Cardiovascular phenotype
Cardiomyopathy
Hypertrophic cardiomyopathy
Intellectual disability
LAMP2-related disorder
Nonpapillary renal cell carcinoma
Primary dilated cardiomyopathy
Trifascicular block on electrocardiogram
Primary familial hypertrophic cardiomyopathy
Melanoma
Thyroid cancer
nonmedullary
1
Malignant tumor of urinary bladder
Isolated Noncompaction of the Ventricular Myocardium
Key Variants
All Variants (169)
RSID Category Clinical Significance Conditions
RS773379092 Health Risk Conflicting classifications of pathogenicity Danon disease, Danon disease
RS773525538 Health Risk Conflicting classifications of pathogenicity Danon disease, Cardiovascular phenotype, Danon disease
RS775032667 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Cardiomyopathy, Danon disease
RS776101722 Health Risk Conflicting classifications of pathogenicity Danon disease, Cardiovascular phenotype, Danon disease
RS777128122 Health Risk Conflicting classifications of pathogenicity Danon disease, Danon disease
RS778577575 Health Risk Conflicting classifications of pathogenicity Danon disease, Cardiovascular phenotype, Danon disease
RS950013593 Health Risk Conflicting classifications of pathogenicity Danon disease, Danon disease
RS1064796635 Health Risk Likely pathogenic Melanoma, Nonpapillary renal cell carcinoma, Melanoma
RS1352584474 Health Risk Likely pathogenic Danon disease, Danon disease, Danon disease
RS1436664364 Health Risk Likely pathogenic Danon disease, Danon disease
RS1602534666 Health Risk Likely pathogenic
RS1602535807 Health Risk Likely pathogenic
RS193922649 Health Risk Likely pathogenic Primary familial hypertrophic cardiomyopathy, Danon disease, Primary familial hypertrophic cardiomyopathy
RS2147281364 Health Risk Likely pathogenic Danon disease, Danon disease
RS2147281483 Health Risk Likely pathogenic Danon disease, Danon disease
RS2147287662 Health Risk Likely pathogenic Cardiomyopathy, Cardiomyopathy
RS2147294820 Health Risk Likely pathogenic Primary dilated cardiomyopathy, Primary dilated cardiomyopathy
RS2147294924 Health Risk Likely pathogenic Danon disease, Danon disease
RS2520912484 Health Risk Likely pathogenic Danon disease, Danon disease
RS2520912530 Health Risk Likely pathogenic Danon disease, Danon disease
RS2520948481 Health Risk Likely pathogenic Danon disease, Danon disease
RS397516739 Health Risk Likely pathogenic Hypertrophic cardiomyopathy, Hypertrophic cardiomyopathy
RS397516752 Health Risk Likely pathogenic Hypertrophic cardiomyopathy, Hypertrophic cardiomyopathy
RS727504262 Health Risk Likely pathogenic Danon disease, Danon disease
RS727504557 Health Risk Likely pathogenic Primary dilated cardiomyopathy, Primary dilated cardiomyopathy
RS730880344 Health Risk Likely pathogenic Danon disease, Hypertrophic cardiomyopathy, Danon disease
RS876657648 Health Risk Likely pathogenic Danon disease, Danon disease
RS104894857 Health Risk Pathogenic Danon disease, Danon disease
RS104894858 Health Risk Pathogenic Danon disease, Hypertrophic cardiomyopathy, Cardiovascular phenotype
RS1060502302 Health Risk Pathogenic Danon disease, Danon disease
RS1060502303 Health Risk Pathogenic Danon disease, Danon disease
RS1060502305 Health Risk Pathogenic Danon disease, Danon disease
RS1060502306 Health Risk Pathogenic Danon disease, Danon disease
RS1183994410 Health Risk Pathogenic Danon disease, Danon disease
RS1271031981 Health Risk Pathogenic Danon disease, Danon disease
RS1327363415 Health Risk Pathogenic Danon disease, Danon disease
RS137852527 Health Risk Pathogenic Danon disease, Danon disease
RS1385890053 Health Risk Pathogenic Danon disease, Danon disease
RS1397410765 Health Risk Pathogenic Danon disease, Danon disease
RS1436181133 Health Risk Pathogenic Danon disease, Danon disease
RS1556092459 Health Risk Pathogenic Danon disease, Danon disease, Danon disease
RS1556101420 Health Risk Pathogenic Danon disease, Danon disease
RS1556101523 Health Risk Pathogenic Danon disease, Cardiovascular phenotype, Danon disease
RS1556123906 Health Risk Pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS1556124149 Health Risk Pathogenic Danon disease, Danon disease, Cardiovascular phenotype
RS1569369194 Health Risk Pathogenic Danon disease, Danon disease
RS1569369940 Health Risk Pathogenic Danon disease, Danon disease
RS1569371330 Health Risk Pathogenic Danon disease, Danon disease
RS1569371591 Health Risk Pathogenic Danon disease, Danon disease
RS1602540152 Health Risk Pathogenic Danon disease, Danon disease
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