| RS1057516262 |
SLC12A6
|
Health Risk |
Pathogenic/Likely pathogenic |
Agenesis of the corpus callosum with peripheral neuropathy, Inborn genetic diseases |
| RS1057516263 |
PKHD1
|
Health Risk |
Likely pathogenic |
Autosomal recessive polycystic kidney disease, Polycystic kidney disease 4 |
| RS1057516264 |
TPP1
|
Health Risk |
Likely pathogenic |
Neuronal ceroid lipofuscinosis 2, Neuronal ceroid lipofuscinosis 2 |
| RS1057516265 |
CHM
|
Health Risk |
Likely pathogenic |
Choroideremia, Choroideremia |
| RS1057516266 |
BBS10
|
Health Risk |
Pathogenic/Likely pathogenic |
Bardet-Biedl syndrome 10, Bardet-Biedl syndrome |
| RS1057516267 |
CLN3
|
Health Risk |
Likely pathogenic |
Neuronal ceroid lipofuscinosis 3, Neuronal ceroid lipofuscinosis 3 |
| RS1057516268 |
PCDH15
|
Health Risk |
Likely pathogenic |
Usher syndrome type 1F, Usher syndrome type 1F |
| RS1057516269 |
HSD17B4
|
Health Risk |
Likely pathogenic |
Bifunctional peroxisomal enzyme deficiency, Perrault syndrome 1 |
| RS1057516270 |
GALC
|
Health Risk |
Conflicting classifications of pathogenicity |
Galactosylceramide beta-galactosidase deficiency, Galactosylceramide beta-galactosidase deficiency |
| RS1057516271 |
SLC12A6
|
Health Risk |
Likely pathogenic |
Agenesis of the corpus callosum with peripheral neuropathy, Agenesis of the corpus callosum with peripheral neuropathy |
| RS1057516272 |
AIRE
|
Health Risk |
Pathogenic |
Polyglandular autoimmune syndrome, type 1 |
| RS1057516273 |
HSD17B4
|
Health Risk |
Likely pathogenic |
Bifunctional peroxisomal enzyme deficiency, Perrault syndrome |
| RS1057516274 |
VPS13B
|
Health Risk |
Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516275 |
GNE
|
Health Risk |
Likely pathogenic |
GNE myopathy, GNE myopathy |
| RS1057516276 |
VPS13B
|
Health Risk |
Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516277 |
GAA
|
Health Risk |
Pathogenic |
Glycogen storage disease, type II |
| RS1057516278 |
ACADM
|
Health Risk |
Pathogenic |
Medium-chain acyl-coenzyme A dehydrogenase deficiency, Medium-chain acyl-coenzyme A dehydrogenase deficiency |
| RS1057516279 |
LAMA3
|
Health Risk |
Likely pathogenic |
Junctional epidermolysis bullosa gravis of Herlitz, Epidermolysis bullosa |
| RS1057516280 |
LAMA3
|
Health Risk |
Likely pathogenic |
Junctional epidermolysis bullosa gravis of Herlitz, Junctional epidermolysis bullosa gravis of Herlitz |
| RS1057516281 |
ABCC8
|
Health Risk |
Pathogenic |
Hyperinsulinemic hypoglycemia, familial |
| RS1057516282 |
ATM
|
Health Risk |
Pathogenic/Likely pathogenic |
Ataxia-telangiectasia syndrome, Hereditary cancer-predisposing syndrome |
| RS1057516283 |
PKHD1
|
Health Risk |
Likely pathogenic |
Autosomal recessive polycystic kidney disease, Polycystic kidney disease 4 |
| RS1057516284 |
VPS13B
|
Health Risk |
Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516285 |
SACS
|
Health Risk |
Likely pathogenic |
Charlevoix-Saguenay spastic ataxia, Charlevoix-Saguenay spastic ataxia |
| RS1057516286 |
MLC1
|
Health Risk |
Likely pathogenic |
Megalencephalic leukoencephalopathy with subcortical cysts 1, Megalencephalic leukoencephalopathy with subcortical cysts 1 |
| RS1057516287 |
VPS13B
|
Health Risk |
Pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516288 |
ARSA
|
Health Risk |
Pathogenic/Likely pathogenic |
Metachromatic leukodystrophy, Metachromatic leukodystrophy |
| RS1057516289 |
MAN2B1
|
Health Risk |
Likely pathogenic |
Deficiency of alpha-mannosidase, Deficiency of alpha-mannosidase |
| RS1057516290 |
GAA
|
Health Risk |
Pathogenic |
Glycogen storage disease, type II |
| RS1057516291 |
FANCC
|
Health Risk |
Pathogenic/Likely pathogenic |
Fanconi anemia complementation group C, Fanconi anemia |
| RS1057516292 |
GRHPR
|
Health Risk |
Likely pathogenic |
Primary hyperoxaluria, type II |
| RS1057516293 |
ALPL
|
Health Risk |
Pathogenic/Likely pathogenic |
Infantile hypophosphatasia, Hypophosphatasia |
| RS1057516294 |
SACS
|
Health Risk |
Likely pathogenic |
Charlevoix-Saguenay spastic ataxia, Charlevoix-Saguenay spastic ataxia |
| RS1057516295 |
SACS
|
Health Risk |
Likely pathogenic |
Charlevoix-Saguenay spastic ataxia, Charlevoix-Saguenay spastic ataxia |
| RS1057516296 |
CTNS
|
Health Risk |
Likely pathogenic |
Nephropathic cystinosis, Nephropathic cystinosis |
| RS1057516297 |
BLM
|
Health Risk |
Likely pathogenic |
Bloom syndrome, Bloom syndrome |
| RS1057516298 |
FANCC
|
Health Risk |
Conflicting classifications of pathogenicity |
Fanconi anemia complementation group C, Fanconi anemia |
| RS1057516299 |
GRHPR
|
Health Risk |
Likely pathogenic |
Primary hyperoxaluria, type II |
| RS1057516300 |
SGCA
|
Health Risk |
Likely pathogenic |
Autosomal recessive limb-girdle muscular dystrophy type 2D, Autosomal recessive limb-girdle muscular dystrophy type 2D |
| RS1057516301 |
ATM
|
Health Risk |
Pathogenic |
Ataxia-telangiectasia syndrome, Hereditary cancer-predisposing syndrome |
| RS1057516302 |
VPS13B
|
Health Risk |
Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516304 |
CPT1A
|
Health Risk |
Likely pathogenic |
Carnitine palmitoyl transferase 1A deficiency, Carnitine palmitoyl transferase 1A deficiency |
| RS1057516305 |
ATP7B
|
Health Risk |
Pathogenic |
Wilson disease, Wilson disease |
| RS1057516306 |
AGL
|
Health Risk |
Pathogenic/Likely pathogenic |
Glycogen storage disease type III, Glycogen storage disease type III |
| RS1057516307 |
HGD
|
Health Risk |
Pathogenic/Likely pathogenic |
Alkaptonuria, Familial prostate cancer |
| RS1057516308 |
AGL
|
Health Risk |
Pathogenic |
Glycogen storage disease type III, Glycogen storage disease type III |
| RS1057516309 |
ASPA
|
Health Risk |
Likely pathogenic |
Spongy degeneration of central nervous system, Spongy degeneration of central nervous system |
| RS1057516310 |
HSD17B4
|
Health Risk |
Likely pathogenic |
Bifunctional peroxisomal enzyme deficiency, Bifunctional peroxisomal enzyme deficiency |
| RS1057516311 |
ATM
|
Health Risk |
Likely pathogenic |
Ataxia-telangiectasia syndrome, Ataxia-telangiectasia syndrome |
| RS1057516312 |
HSD17B4
|
Health Risk |
Pathogenic |
Bifunctional peroxisomal enzyme deficiency, Bifunctional peroxisomal enzyme deficiency |
| RS1057516313 |
FANCC
|
Health Risk |
Likely pathogenic |
Fanconi anemia complementation group C, Fanconi anemia complementation group C |
| RS1057516314 |
AIRE
|
Health Risk |
Likely pathogenic |
Polyglandular autoimmune syndrome, type 1 |
| RS1057516315 |
ASPA
|
Health Risk |
Pathogenic |
Spongy degeneration of central nervous system, Canavan Disease |
| RS1057516316 |
LAMB3
|
Health Risk |
Likely pathogenic |
Junctional epidermolysis bullosa gravis of Herlitz, Junctional epidermolysis bullosa gravis of Herlitz |
| RS1057516317 |
ABCC8
|
Health Risk |
Pathogenic |
Hyperinsulinemic hypoglycemia, familial |
| RS1057516318 |
POMGNT1
|
Health Risk |
Likely pathogenic |
Muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A3 |
| RS1057516319 |
TPP1
|
Health Risk |
Pathogenic |
Neuronal ceroid lipofuscinosis 2, Abnormality of the nervous system |
| RS1057516320 |
NBN
|
Health Risk |
Pathogenic/Likely pathogenic |
Microcephaly, normal intelligence and immunodeficiency |
| RS1057516323 |
PMM2
|
Health Risk |
Pathogenic |
PMM2-congenital disorder of glycosylation, See cases |
| RS1057516324 |
VPS13B
|
Health Risk |
Pathogenic/Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516325 |
MAN2B1
|
Health Risk |
Likely pathogenic |
Deficiency of alpha-mannosidase, Deficiency of alpha-mannosidase |
| RS1057516326 |
HADHA
|
Health Risk |
Pathogenic |
Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency, Mitochondrial trifunctional protein deficiency |
| RS1057516327 |
GAA
|
Health Risk |
Pathogenic |
Glycogen storage disease, type II |
| RS1057516328 |
GAA
|
Health Risk |
Pathogenic |
Glycogen storage disease, type II |
| RS1057516329 |
PYGM
|
Health Risk |
Pathogenic/Likely pathogenic |
Glycogen storage disease, type V |
| RS1057516330 |
BBS1
|
Health Risk |
Likely pathogenic |
Bardet-Biedl syndrome 1, Bardet-Biedl syndrome 1 |
| RS1057516331 |
VPS13B
|
Health Risk |
Likely pathogenic |
Cohen syndrome, Cohen syndrome |
| RS1057516332 |
NBN
|
Health Risk |
Pathogenic |
Microcephaly, normal intelligence and immunodeficiency |
| RS1057516333 |
FAH
|
Health Risk |
Likely pathogenic |
Tyrosinemia type I, Tyrosinemia type I |
| RS1057516334 |
ALPL
|
Health Risk |
Pathogenic |
Infantile hypophosphatasia, Adult hypophosphatasia |
| RS1057516335 |
CLN3
|
Health Risk |
Pathogenic |
Neuronal ceroid lipofuscinosis 3, Neuronal ceroid lipofuscinosis |
| RS1057516336 |
MLC1
|
Health Risk |
Likely pathogenic |
Megalencephalic leukoencephalopathy with subcortical cysts 1, Megalencephalic leukoencephalopathy with subcortical cysts 1 |
| RS1057516337 |
SLC12A6
|
Health Risk |
Likely pathogenic |
Agenesis of the corpus callosum with peripheral neuropathy, Charcot-Marie-Tooth disease |
| RS1057516338 |
ASS1
|
Health Risk |
Pathogenic |
Citrullinemia type I, Citrullinemia |
| RS1057516339 |
ASS1
|
Health Risk |
Pathogenic |
Citrullinemia type I, Citrullinemia |
| RS1057516340 |
GNE
|
Health Risk |
Likely pathogenic |
GNE myopathy, GNE myopathy |
| RS1057516341 |
GAA
|
Health Risk |
Likely pathogenic |
Glycogen storage disease, type II |
| RS1057516342 |
PCDH15
|
Health Risk |
Pathogenic |
Autosomal recessive nonsyndromic hearing loss 23, Usher syndrome type 1F |
| RS1057516343 |
CLN3
|
Health Risk |
Likely pathogenic |
Neuronal ceroid lipofuscinosis 3, Neuronal ceroid lipofuscinosis |
| RS1057516344 |
GCDH
|
Health Risk |
Pathogenic |
Glutaric aciduria, type 1 |
| RS1057516345 |
PKHD1
|
Health Risk |
Pathogenic |
Autosomal recessive polycystic kidney disease, Polycystic kidney disease 4 |
| RS1057516346 |
BCS1L
|
Health Risk |
Likely pathogenic |
GRACILE syndrome, Mitochondrial complex III deficiency nuclear type 1 |
| RS1057516347 |
SACS
|
Health Risk |
Likely pathogenic |
Charlevoix-Saguenay spastic ataxia, Charlevoix-Saguenay spastic ataxia |
| RS1057516348 |
NEB
|
Health Risk |
Likely pathogenic |
Nemaline myopathy 2, Nemaline myopathy 2 |
| RS1057516349 |
PYGM
|
Health Risk |
Pathogenic/Likely pathogenic |
Glycogen storage disease, type V |
| RS1057516350 |
HADHA
|
Health Risk |
Likely pathogenic |
Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency, Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency |
| RS1057516351 |
PCDH15
|
Health Risk |
Likely pathogenic |
Usher syndrome type 1F, Usher syndrome type 1F |
| RS1057516352 |
HGD
|
Health Risk |
Likely pathogenic |
Alkaptonuria, Alkaptonuria |
| RS1057516354 |
SLC26A4
|
Health Risk |
Pathogenic |
Pendred syndrome, Pendred syndrome |
| RS1057516355 |
HGD
|
Health Risk |
Pathogenic |
Alkaptonuria, Alkaptonuria |
| RS1057516356 |
DPYD
|
Health Risk |
Likely pathogenic |
Dihydropyrimidine dehydrogenase deficiency, Dihydropyrimidine dehydrogenase deficiency |
| RS1057516357 |
DPYD
|
Health Risk |
Likely pathogenic |
Dihydropyrimidine dehydrogenase deficiency, Dihydropyrimidine dehydrogenase deficiency |
| RS1057516358 |
ATM
|
Health Risk |
Likely pathogenic |
Ataxia-telangiectasia syndrome, Ataxia-telangiectasia syndrome |
| RS1057516360 |
SGCB
|
Health Risk |
Likely pathogenic |
Autosomal recessive limb-girdle muscular dystrophy type 2E, Autosomal recessive limb-girdle muscular dystrophy type 2E |
| RS1057516361 |
BLM
|
Health Risk |
Pathogenic |
Bloom syndrome, Bloom syndrome |
| RS1057516362 |
HGD
|
Health Risk |
Pathogenic/Likely pathogenic |
Alkaptonuria, Alkaptonuria |
| RS1057516363 |
GAA
|
Health Risk |
Pathogenic |
Glycogen storage disease, type II |
| RS1057516364 |
GNE
|
Health Risk |
Likely pathogenic |
GNE myopathy, Sialuria |
| RS1057516365 |
SACS
|
Health Risk |
Pathogenic/Likely pathogenic |
Charlevoix-Saguenay spastic ataxia, Spastic paraplegia |
| RS1057516366 |
TPP1
|
Health Risk |
Pathogenic |
Neuronal ceroid lipofuscinosis 2, Neuronal ceroid lipofuscinosis 2 |