SYT2 Chromosome 1

Synaptotagmin 2
21 variants 21 Health Risk

Upload your DNA to see your personal genotypes for variants in SYT2.

What This Gene Does
This gene encodes a synaptic vesicle membrane protein. The encoded protein is thought to function as a calcium sensor in vesicular trafficking and exocytosis. Mutations in this gene are associated with myasthenic syndrome, presynaptic, congenital, with or without motor neuropathy. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Oct 2014]
Gene Info
Gene Group
Synaptotagmins
Locus Type
gene with protein product
Location
1q32.1
Ensembl
ENSG00000143858
Associated Conditions (10)
Congenital myasthenic syndrome 7
Inborn genetic diseases
Muscle weakness
Respiratory distress
SYT2-related disorder
Myasthenic syndrome
congenital
7B
presynaptic
autosomal recessive
Key Variants
All Variants (21)
RSID Category Clinical Significance Conditions
RS142804180 Health Risk Conflicting classifications of pathogenicity
RS1690515734 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
RS199582045 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS587777782 Health Risk Conflicting classifications of pathogenicity Congenital myasthenic syndrome 7, Inborn genetic diseases, Congenital myasthenic syndrome 7
RS752537599 Health Risk Conflicting classifications of pathogenicity
RS780359132 Health Risk Conflicting classifications of pathogenicity
RS1057518805 Health Risk Likely pathogenic Muscle weakness, Respiratory distress, Muscle weakness
RS1690455297 Health Risk Likely pathogenic
RS1690636110 Health Risk Likely pathogenic SYT2-related disorder, SYT2-related disorder
RS2149066990 Health Risk Likely pathogenic
RS2526974512 Health Risk Likely pathogenic Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
RS2526989632 Health Risk Likely pathogenic Myasthenic syndrome, congenital, 7B
RS1690318147 Health Risk Pathogenic Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
RS2149063864 Health Risk Pathogenic Myasthenic syndrome, congenital, 7B
RS2149063996 Health Risk Pathogenic Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
RS2149064005 Health Risk Pathogenic Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
RS2149067131 Health Risk Pathogenic Myasthenic syndrome, congenital, 7B
RS2149068434 Health Risk Pathogenic Myasthenic syndrome, congenital, 7B
RS2149069543 Health Risk Pathogenic Myasthenic syndrome, congenital, 7B
RS2526969474 Health Risk Pathogenic
RS587777781 Health Risk Pathogenic Congenital myasthenic syndrome 7, Congenital myasthenic syndrome 7
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