SLC2A1 Chromosome 1

Solute carrier family 2 member 1
346 variants 346 Health Risk

Upload your DNA to see your personal genotypes for variants in SLC2A1.

What This Gene Does
This gene encodes a major glucose transporter in the mammalian blood-brain barrier. The encoded protein is found primarily in the cell membrane and on the cell surface, where it can also function as a receptor for human T-cell leukemia virus (HTLV) I and II. Mutations in this gene have been found in a family with paroxysmal exertion-induced dyskinesia. [provided by RefSeq, Apr 2013]
Gene Info
Gene Group
Solute carrier family 2
Locus Type
gene with protein product
Location
1p34.2
Ensembl
ENSG00000117394
Associated Conditions (34)
GLUT1 deficiency syndrome 1
autosomal recessive
Encephalopathy due to GLUT1 deficiency
Hereditary cryohydrocytosis with reduced stomatin
Childhood onset GLUT1 deficiency syndrome 2
Dystonia 9
Epilepsy
idiopathic generalized
susceptibility to
12
SLC2A1-related disorder
Inborn genetic diseases
Gastric cancer
Beckwith-Wiedemann syndrome
Intellectual disability
Seizure
Developmental disorder
See cases
Parkinsonian disorder
Paroxysmal dystonia
+14 more conditions
Key Variants
RS1064795363
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
Health Risk
RS1085308009
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
Health Risk
RS1181822928
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, SLC2A1-related disorder
Health Risk
RS1387242348
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Inborn genetic diseases
Health Risk
RS139412383
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Epilepsy
Health Risk
RS139492241
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Inborn genetic diseases
Health Risk
RS140825318
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Inborn genetic diseases
Health Risk
RS141619735
Conflicting classifications of pathogenicity
Hereditary cryohydrocytosis with reduced stomatin, Epilepsy, idiopathic generalized
Health Risk
RS1425773776
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Encephalopathy due to GLUT1 deficiency
Health Risk
RS142986731
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, Beckwith-Wiedemann syndrome
Health Risk
RS143588685
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
Health Risk
RS147249343
Conflicting classifications of pathogenicity
GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
Health Risk
All Variants (346)
RSID Category Clinical Significance Conditions
RS1643484447 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS1643807832 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124445408 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124445519 Health Risk Pathogenic Encephalopathy due to GLUT1 deficiency, Encephalopathy due to GLUT1 deficiency
RS2124445661 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124446209 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124446266 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124446296 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124446305 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124446431 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124446490 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124447951 Health Risk Pathogenic Childhood onset GLUT1 deficiency syndrome 2, Childhood onset GLUT1 deficiency syndrome 2
RS2124447989 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448063 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, Encephalopathy due to GLUT1 deficiency
RS2124448369 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448402 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448406 Health Risk Pathogenic Childhood onset GLUT1 deficiency syndrome 2, Childhood onset GLUT1 deficiency syndrome 2
RS2124448423 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448836 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448851 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124448988 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124449015 Health Risk Pathogenic Dystonia 9, Encephalopathy due to GLUT1 deficiency, Dystonia 9
RS2124449099 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124449259 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124449287 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124449299 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, Encephalopathy due to GLUT1 deficiency
RS2124449417 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, Inborn genetic diseases
RS2124450060 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450132 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450179 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450273 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450330 Health Risk Pathogenic
RS2124450420 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450471 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450697 Health Risk Pathogenic Encephalopathy due to GLUT1 deficiency, GLUT1 deficiency syndrome 1, autosomal recessive
RS2124450705 Health Risk Pathogenic Encephalopathy due to GLUT1 deficiency, Encephalopathy due to GLUT1 deficiency
RS2124450806 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450914 Health Risk Pathogenic
RS2124450939 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2124450950 Health Risk Pathogenic Dystonia 9, Encephalopathy due to GLUT1 deficiency, Encephalopathy due to GLUT1 deficiency
RS2124461790 Health Risk Pathogenic
RS2124461913 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124461926 Health Risk Pathogenic Dystonia 9, Dystonia 9
RS2124478725 Health Risk Pathogenic Dystonia 9, Encephalopathy due to GLUT1 deficiency, Inborn genetic diseases
RS2524982606 Health Risk Pathogenic SLC2A1-related disorder, SLC2A1-related disorder
RS2524984262 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2524984323 Health Risk Pathogenic
RS2524984541 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
RS2524984571 Health Risk Pathogenic
RS2524984688 Health Risk Pathogenic GLUT1 deficiency syndrome 1, autosomal recessive, GLUT1 deficiency syndrome 1
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