IGF1R Chromosome 15

Insulin like growth factor 1 receptor
104 variants 98 Health Risk 6 Protective

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What This Gene Does
This receptor binds insulin-like growth factor with a high affinity. It has tyrosine kinase activity. The insulin-like growth factor I receptor plays a critical role in transformation events. Cleavage of the precursor generates alpha and beta subunits. It is highly overexpressed in most malignant tissues where it functions as an anti-apoptotic agent by enhancing cell survival. Alternatively spliced transcript variants encoding distinct isoforms have been found for this gene. [provided by RefSeq, May 2014]
Gene Info
Gene Group
"CD molecules|Fibronectin type III domain containing|MicroRNA protein coding host genes|Insulin receptor family"
Locus Type
gene with protein product
Location
15q26.3
Ensembl
ENSG00000140443
Associated Conditions (7)
Growth delay due to insulin-like growth factor I resistance
IGF1R-related disorder
Inborn genetic diseases
NK-cell enteropathy
Neurodevelopmental disorder
Microcephaly
Intellectual disability
Key Variants
RS117440569
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, IGF1R-related disorder, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS1250642880
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS141802822
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS144739747
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, IGF1R-related disorder, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS145668206
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS146902252
Conflicting classifications of pathogenicity
Health Risk
RS149417802
Conflicting classifications of pathogenicity
Health Risk
RS1596476159
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Inborn genetic diseases, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS200261849
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS200740840
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS201351992
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
RS202060277
Conflicting classifications of pathogenicity
Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
Health Risk
All Variants (104)
RSID Category Clinical Significance Conditions
RS886044448 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS9282723 Health Risk Conflicting classifications of pathogenicity
RS1064793151 Health Risk Likely pathogenic
RS1131691583 Health Risk Likely pathogenic IGF1R-related disorder, IGF1R-related disorder
RS1448143895 Health Risk Likely pathogenic IGF1R-related disorder, IGF1R-related disorder
RS1555434208 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596214066 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596409872 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596468621 Health Risk Likely pathogenic
RS1596468719 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596476061 Health Risk Likely pathogenic NK-cell enteropathy, NK-cell enteropathy
RS1596476163 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2014223788 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2141155238 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS2151681264 Health Risk Likely pathogenic Microcephaly, Growth delay due to insulin-like growth factor I resistance, Microcephaly
RS2151694492 Health Risk Likely pathogenic
RS2151726658 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2505321709 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2506023488 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS2506059210 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS2506069523 Health Risk Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2506091121 Health Risk Likely pathogenic
RS886042346 Health Risk Likely pathogenic
RS1057524426 Health Risk Pathogenic
RS1322503729 Health Risk Pathogenic Inborn genetic diseases, Growth delay due to insulin-like growth factor I resistance, Inborn genetic diseases
RS1555460702 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1555462145 Health Risk Pathogenic
RS1555463008 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1567197213 Health Risk Pathogenic
RS1596214576 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596413181 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1596457128 Health Risk Pathogenic
RS2013914972 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2016082493 Health Risk Pathogenic
RS2141155132 Health Risk Pathogenic
RS2151690905 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2151708486 Health Risk Pathogenic
RS2505514642 Health Risk Pathogenic
RS2505969779 Health Risk Pathogenic
RS2505981458 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS2506014488 Health Risk Pathogenic
RS2506034722 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS746570875 Health Risk Pathogenic
RS774794966 Health Risk Pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS1173681603 Health Risk Pathogenic/Likely pathogenic Intellectual disability, Growth delay due to insulin-like growth factor I resistance, Intellectual disability
RS1596472892 Health Risk Pathogenic/Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS2151652750 Health Risk Pathogenic/Likely pathogenic Intellectual disability, Growth delay due to insulin-like growth factor I resistance, Intellectual disability
RS2506058863 Health Risk Pathogenic/Likely pathogenic Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS121912426 Protective protective Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
RS121912427 Protective protective Growth delay due to insulin-like growth factor I resistance, Growth delay due to insulin-like growth factor I resistance
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