HIVEP2 Chromosome 6

HIVEP zinc finger 2
118 variants 118 Health Risk

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What This Gene Does
This gene encodes a member of a family of closely related, large, zinc finger-containing transcription factors. The encoded protein regulates transcription by binding to regulatory regions of various cellular and viral genes that maybe involved in growth, development and metastasis. The protein contains the ZAS domain comprised of two widely separated regions of zinc finger motifs, a stretch of highly acidic amino acids and a serine/threonine-rich sequence. [provided by RefSeq, Nov 2012]
Gene Info
Gene Group
Zinc fingers C2H2-type
Locus Type
gene with protein product
Location
6q24.2
Ensembl
ENSG00000010818
Associated Conditions (7)
Inborn genetic diseases
Intellectual disability
autosomal dominant 43
HIVEP2-related disorder
Congenital ocular coloboma
Angelman syndrome-like
Neurodevelopmental delay
Key Variants
All Variants (118)
RSID Category Clinical Significance Conditions
RS765561928 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS765612030 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS768721723 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Intellectual disability, autosomal dominant 43
RS768763368 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS770827886 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS777382930 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 43, Intellectual disability
RS777898357 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS779169052 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS780128851 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 43, Inborn genetic diseases
RS868085949 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS921397256 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS951703772 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 43, Inborn genetic diseases
RS974381338 Health Risk Conflicting classifications of pathogenicity
RS994493921 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS999634501 Health Risk Conflicting classifications of pathogenicity
RS1064795825 Health Risk Likely pathogenic
RS1474776725 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1554275655 Health Risk Likely pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1582842733 Health Risk Likely pathogenic
RS1774993424 Health Risk Likely pathogenic Intellectual disability, Intellectual disability
RS1775173231 Health Risk Likely pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1775234925 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1775510548 Health Risk Likely pathogenic Intellectual disability, Intellectual disability
RS2482796579 Health Risk Likely pathogenic HIVEP2-related disorder, HIVEP2-related disorder
RS2482811651 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2482820753 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2482829253 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2482835597 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2482839679 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2482859580 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1064796034 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1554274371 Health Risk Pathogenic Inborn genetic diseases, Intellectual disability, autosomal dominant 43
RS1554275163 Health Risk Pathogenic Angelman syndrome-like, Intellectual disability, autosomal dominant 43
RS1562493608 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1562505335 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1562505675 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1582831184 Health Risk Pathogenic
RS1582831406 Health Risk Pathogenic
RS1582842042 Health Risk Pathogenic
RS1582843150 Health Risk Pathogenic Angelman syndrome-like, Angelman syndrome-like
RS1774993567 Health Risk Pathogenic
RS1775199259 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1775202280 Health Risk Pathogenic
RS1775204653 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS1775623278 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2114611238 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2114611483 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2114611687 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2114653975 Health Risk Pathogenic Intellectual disability, autosomal dominant 43, Intellectual disability
RS2114664519 Health Risk Pathogenic Neurodevelopmental delay, Neurodevelopmental delay
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