BRCA1 Chromosome 17
BRCA1 DNA repair associated
Upload your DNA to see your personal genotypes for variants in BRCA1.
What This Gene Does
This gene encodes a 190 kD nuclear phosphoprotein that plays a role in maintaining genomic stability, and it also acts as a tumor suppressor. The BRCA1 gene contains 22 exons spanning about 110 kb of DNA. The encoded protein combines with other tumor suppressors, DNA damage sensors, and signal transducers to form a large multi-subunit protein complex known as the BRCA1-associated genome surveillance complex (BASC). This gene product associates with RNA polymerase II, and through the C-terminal domain, also interacts with histone deacetylase complexes. This protein thus plays a role in transcription, DNA repair of double-stranded breaks, and recombination. Mutations in this gene are responsible for approximately 40% of inherited breast cancers and more than 80% of inherited breast and ovarian cancers. Alternative splicing plays a role in modulating the subcellular localization and physiological function of this gene. Many alternatively spliced transcript variants, some of which are disease-associated mutations, have been described for this gene, but the full-length natures of only some of these variants has been described. A related pseudogene, which is also located on chromosome 17, has been identified. [provided by RefSeq, May 2020]
Gene Info
Gene Group
"Ring finger proteins|FA complementation groups|Protein phosphatase 1 regulatory subunits|BRCA1 A complex|BRCA1 B complex|BRCA1 C complex"
Locus Type
gene with protein product
Location
17q21.31
Ensembl
ENSG00000012048
Associated Conditions (66)
Hereditary cancer-predisposing syndrome
Hereditary breast ovarian cancer syndrome
Malignant tumor of breast
BRCA1-related disorder
Breast-ovarian cancer
familial
susceptibility to
1
Fanconi anemia
complementation group S
Familial cancer of breast
Pancreatic cancer
4
BRCA1-related cancer predisposition
Hereditary cancer
Breast and/or ovarian cancer
Breast cancer
Inherited breast cancer and ovarian cancer
2
Familial pancreatic carcinoma
+46 more conditions
Key Variants
RS1011096937
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary breast ovarian cancer syndrome, Malignant tumor of breast
Health Risk
RS1015073230
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome
Health Risk
RS1022076404
Conflicting classifications of pathogenicity
Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome, BRCA1-related disorder
Health Risk
RS1029207537
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome
Health Risk
RS1036328075
Conflicting classifications of pathogenicity
Breast-ovarian cancer, familial, susceptibility to
Health Risk
RS1038244014
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary cancer-predisposing syndrome
Health Risk
RS1050289746
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome
Health Risk
RS1055368753
Conflicting classifications of pathogenicity
Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome, Hereditary breast ovarian cancer syndrome
Health Risk
RS1057519249
Conflicting classifications of pathogenicity
Breast-ovarian cancer, familial, susceptibility to
Health Risk
RS1057519495
Conflicting classifications of pathogenicity
Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial
Health Risk
RS1057519496
Conflicting classifications of pathogenicity
Hereditary breast ovarian cancer syndrome, Hereditary cancer-predisposing syndrome, Breast-ovarian cancer
Health Risk
RS1057520246
Conflicting classifications of pathogenicity
Hereditary cancer-predisposing syndrome, Hereditary cancer-predisposing syndrome
Health Risk
All Variants (5374)
| RSID | Category | Clinical Significance | Conditions |
|---|---|---|---|
| RS80357860 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357861 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357863 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357864 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357865 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357867 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357868 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357869 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357870 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357871 | Health Risk | Pathogenic | Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial |
| RS80357872 | Health Risk | Pathogenic | Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial |
| RS80357874 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357876 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357877 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357878 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357879 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357880 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357881 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357882 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357883 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357884 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357885 | Health Risk | Pathogenic | Familial cancer of breast, Breast-ovarian cancer, familial |
| RS80357886 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357887 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357888 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357890 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357892 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357893 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357894 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357895 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357896 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357897 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357899 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357900 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357901 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357902 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357904 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357905 | Health Risk | Pathogenic | Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial |
| RS80357906 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357907 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357908 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357909 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357912 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357913 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357914 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357915 | Health Risk | Pathogenic | Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial |
| RS80357916 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357918 | Health Risk | Pathogenic | Hereditary breast ovarian cancer syndrome, Breast-ovarian cancer, familial |
| RS80357919 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |
| RS80357920 | Health Risk | Pathogenic | Breast-ovarian cancer, familial, susceptibility to |