ZFHX2 Chromosome 14

Zinc finger homeobox 2
13 variants 13 Health Risk

Upload your DNA to see your personal genotypes for variants in ZFHX2.

What This Gene Does
Predicted to enable DNA-binding transcription factor activity, RNA polymerase II-specific and RNA polymerase II cis-regulatory region sequence-specific DNA binding activity. Involved in regulation of sensory perception of pain. Located in nucleus. Implicated in Marsili syndrome. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
"Zinc fingers C2H2-type|Zinc fingers matrin-type|ZF class homeoboxes and pseudogenes"
Locus Type
gene with protein product
Location
14q11.2
Ensembl
ENSG00000136367
Associated Conditions (4)
Indifference to pain
congenital
autosomal dominant
ZFHX2-related disorder
Key Variants
All Variants (13)
RSID Category Clinical Significance Conditions
RS1055701850 Health Risk Conflicting classifications of pathogenicity
RS1220815012 Health Risk Conflicting classifications of pathogenicity
RS201801159 Health Risk Conflicting classifications of pathogenicity Indifference to pain, congenital, autosomal dominant
RS368892129 Health Risk Conflicting classifications of pathogenicity
RS527943085 Health Risk Conflicting classifications of pathogenicity
RS540160949 Health Risk Conflicting classifications of pathogenicity
RS543843286 Health Risk Conflicting classifications of pathogenicity
RS566246733 Health Risk Conflicting classifications of pathogenicity
RS566304076 Health Risk Conflicting classifications of pathogenicity
RS575221770 Health Risk Conflicting classifications of pathogenicity ZFHX2-related disorder, ZFHX2-related disorder
RS773850439 Health Risk Conflicting classifications of pathogenicity
RS780826119 Health Risk Conflicting classifications of pathogenicity
RS1555344723 Health Risk Pathogenic Indifference to pain, congenital, autosomal dominant
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