UBAP1 Chromosome 9

Ubiquitin associated protein 1
16 variants 16 Health Risk

Upload your DNA to see your personal genotypes for variants in UBAP1.

What This Gene Does
This gene is a member of the UBA domain family, whose members include proteins having connections to ubiquitin and the ubiquitination pathway. The ubiquitin associated domain is thought to be a non-covalent ubiquitin binding domain consisting of a compact three helix bundle. This particular protein originates from a gene locus in a refined region on chromosome 9 undergoing loss of heterozygosity in nasopharyngeal carcinoma (NPC). Taking into account its cytogenetic location, this UBA domain family member is being studies as a putative target for mutation in nasopharyngeal carcinomas. Multiple alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jan 2010]
Gene Info
Gene Group
ESCRT-I
Locus Type
gene with protein product
Location
9p13.3
Ensembl
ENSG00000165006
Associated Conditions (5)
Inborn genetic diseases
Spastic paraplegia 80
autosomal dominant
UBAP1-related disorder
Hereditary spastic paraplegia
Key Variants
All Variants (16)
RSID Category Clinical Significance Conditions
RS146620671 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Spastic paraplegia 80, autosomal dominant
RS370655695 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS562285027 Health Risk Conflicting classifications of pathogenicity UBAP1-related disorder, UBAP1-related disorder
RS1227081826 Health Risk Likely pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1563919973 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1563920000 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1563920132 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1563920172 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1563920252 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Hereditary spastic paraplegia
RS1563920268 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1587878722 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1587878961 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1587879449 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS2131620305 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS2491080250 Health Risk Pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
RS1833955862 Health Risk Pathogenic/Likely pathogenic Spastic paraplegia 80, autosomal dominant, Spastic paraplegia 80
Sign Up to Analyze Your DNA Log In