TYMP Chromosome 22

Thymidine phosphorylase
191 variants 191 Health Risk

Upload your DNA to see your personal genotypes for variants in TYMP.

What This Gene Does
This gene encodes an angiogenic factor which promotes angiogenesis in vivo and stimulates the in vitro growth of a variety of endothelial cells. It has a highly restricted target cell specificity acting only on endothelial cells. Mutations in this gene have been associated with mitochondrial neurogastrointestinal encephalomyopathy. Multiple alternatively spliced transcript variants have been identified. [provided by RefSeq, Apr 2012]
Gene Info
Gene Group
Minor histocompatibility antigens
Locus Type
gene with protein product
Location
22q13.33
Ensembl
ENSG00000025708
Associated Conditions (8)
Mitochondrial DNA depletion syndrome 1
TYMP-related disorder
Mitochondrial neurogastrointestinal encephalomyopathy
Inborn genetic diseases
Intestinal pseudo-obstruction
Thyroid cancer
nonmedullary
1
Key Variants
RS1064792873
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS121913042
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS143789597
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, TYMP-related disorder, Mitochondrial DNA depletion syndrome 1
Health Risk
RS146922557
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS188802138
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial neurogastrointestinal encephalomyopathy, Mitochondrial DNA depletion syndrome 1
Health Risk
RS200497106
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS200818286
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS369574115
Conflicting classifications of pathogenicity
Health Risk
RS372421189
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial neurogastrointestinal encephalomyopathy, TYMP-related disorder
Health Risk
RS372620403
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS372690172
Conflicting classifications of pathogenicity
Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
Health Risk
RS377497287
Conflicting classifications of pathogenicity
Mitochondrial neurogastrointestinal encephalomyopathy, Mitochondrial DNA depletion syndrome 1, TYMP-related disorder
Health Risk
All Variants (191)
RSID Category Clinical Significance Conditions
RS2522550898 Health Risk Pathogenic
RS2522551059 Health Risk Pathogenic
RS2522551530 Health Risk Pathogenic
RS2522551571 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2522551905 Health Risk Pathogenic
RS28931613 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS367723039 Health Risk Pathogenic
RS374043253 Health Risk Pathogenic
RS749827433 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS761608162 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS761665644 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS764275775 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS767245071 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial neurogastrointestinal encephalomyopathy, Mitochondrial DNA depletion syndrome 1
RS770277446 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS778914092 Health Risk Pathogenic
RS786205097 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS797044454 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial neurogastrointestinal encephalomyopathy, TYMP-related disorder
RS866001342 Health Risk Pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS867787320 Health Risk Pathogenic
RS893130646 Health Risk Pathogenic
RS1027855768 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS1052593047 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS1180285291 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS1200526412 Health Risk Pathogenic/Likely pathogenic TYMP-related disorder, TYMP-related disorder
RS1203886148 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS121913037 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial neurogastrointestinal encephalomyopathy, Mitochondrial DNA depletion syndrome 1
RS121913039 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS1295236603 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2069377278 Health Risk Pathogenic/Likely pathogenic
RS2069446068 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2069504242 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2148683541 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2522513131 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2522546758 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS2522546966 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS755728248 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS760629248 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS764792655 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS765023287 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS767575537 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
RS891107196 Health Risk Pathogenic/Likely pathogenic Mitochondrial DNA depletion syndrome 1, Mitochondrial DNA depletion syndrome 1
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