TTLL5 Chromosome 14

Tubulin tyrosine ligase like 5
98 variants 98 Health Risk

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What This Gene Does
This gene encodes a member of the tubulin tyrosine ligase like protein family. This protein interacts with two glucocorticoid receptor coactivators, transcriptional intermediary factor 2 and steroid receptor coactivator 1. This protein may function as a coregulator of glucocorticoid receptor mediated gene induction and repression. This protein may also function as an alpha tubulin polyglutamylase.[provided by RefSeq, Feb 2010]
Gene Info
Gene Group
Tubulin tyrosine ligase family
Locus Type
gene with protein product
Location
14q24.3
Ensembl
ENSG00000119685
Associated Conditions (9)
Cone-rod dystrophy 19
Inborn genetic diseases
Retinal dystrophy
TTLL5-related disorder
Ovarian serous cystadenocarcinoma
Cone-rod dystrophy
Colon adenocarcinoma
Central areolar choroidal dystrophy
Retinitis pigmentosa
Key Variants
All Variants (98)
RSID Category Clinical Significance Conditions
RS142169707 Health Risk Conflicting classifications of pathogenicity
RS142465256 Health Risk Conflicting classifications of pathogenicity Cone-rod dystrophy 19, Cone-rod dystrophy 19
RS17849666 Health Risk Conflicting classifications of pathogenicity
RS185326652 Health Risk Conflicting classifications of pathogenicity
RS189135452 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS2503347872 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS573319891 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS753057666 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS765401548 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS772723003 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS778408194 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS781316021 Health Risk Conflicting classifications of pathogenicity TTLL5-related disorder, Retinal dystrophy, TTLL5-related disorder
RS896484588 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1192053295 Health Risk Likely pathogenic
RS1194072973 Health Risk Likely pathogenic
RS1206062558 Health Risk Likely pathogenic
RS1314926139 Health Risk Likely pathogenic
RS1359166382 Health Risk Likely pathogenic
RS1887579263 Health Risk Likely pathogenic Retinal dystrophy, Ovarian serous cystadenocarcinoma, Retinal dystrophy
RS1891341077 Health Risk Likely pathogenic
RS2140155252 Health Risk Likely pathogenic
RS2503134087 Health Risk Likely pathogenic
RS2503293795 Health Risk Likely pathogenic Cone-rod dystrophy, Cone-rod dystrophy
RS2503294089 Health Risk Likely pathogenic
RS2504286530 Health Risk Likely pathogenic TTLL5-related disorder, TTLL5-related disorder
RS752669828 Health Risk Likely pathogenic
RS756311924 Health Risk Likely pathogenic
RS766173950 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS778757743 Health Risk Likely pathogenic
RS779740894 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS867401129 Health Risk Likely pathogenic Colon adenocarcinoma, Colon adenocarcinoma
RS886043466 Health Risk Likely pathogenic
RS990308427 Health Risk Likely pathogenic
RS1034395084 Health Risk Pathogenic
RS1163242822 Health Risk Pathogenic
RS1193187457 Health Risk Pathogenic
RS1309614617 Health Risk Pathogenic
RS1324798326 Health Risk Pathogenic
RS1340982465 Health Risk Pathogenic
RS138370992 Health Risk Pathogenic Cone-rod dystrophy 19, Retinal dystrophy, Cone-rod dystrophy 19
RS140018292 Health Risk Pathogenic
RS1400806789 Health Risk Pathogenic Central areolar choroidal dystrophy, Retinal dystrophy, Central areolar choroidal dystrophy
RS1408235770 Health Risk Pathogenic
RS1555345387 Health Risk Pathogenic Cone-rod dystrophy 19, Cone-rod dystrophy 19
RS1566585766 Health Risk Pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1566831299 Health Risk Pathogenic
RS1595009158 Health Risk Pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1883546949 Health Risk Pathogenic
RS1887780037 Health Risk Pathogenic
RS1890963211 Health Risk Pathogenic
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