TRPM6 Chromosome 9

Transient receptor potential cation channel subfamily M member 6
71 variants 71 Health Risk

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What This Gene Does
This gene is predominantly expressed in the kidney and colon, and encodes a protein containing an ion channel domain and a protein kinase domain. It is crucial for magnesium homeostasis, and plays an essential role in epithelial magnesium transport and in the active magnesium absorption in the gut and kidney. Mutations in this gene are associated with hypomagnesemia with secondary hypocalcemia. Alternatively spliced transcript variants encoding different isoforms have been noted for this gene. [provided by RefSeq, Apr 2010]
Gene Info
Gene Group
"Transient receptor potential cation channels|Alpha kinases"
Locus Type
gene with protein product
Location
9q21.13
Ensembl
ENSG00000119121
Associated Conditions (3)
Intestinal hypomagnesemia 1
TRPM6-related disorder
Inborn genetic diseases
Key Variants
RS113003674
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS114160749
Conflicting classifications of pathogenicity
Health Risk
RS1252685523
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS138880537
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS140835112
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
Health Risk
RS141014694
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS141809291
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS142043309
Conflicting classifications of pathogenicity
TRPM6-related disorder, Inborn genetic diseases, TRPM6-related disorder
Health Risk
RS142946646
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS143164660
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
Health Risk
RS1472189003
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
Health Risk
RS147635290
Conflicting classifications of pathogenicity
Intestinal hypomagnesemia 1, Inborn genetic diseases, Intestinal hypomagnesemia 1
Health Risk
All Variants (71)
RSID Category Clinical Significance Conditions
RS113003674 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS114160749 Health Risk Conflicting classifications of pathogenicity
RS1252685523 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS138880537 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS140835112 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
RS141014694 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS141809291 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS142043309 Health Risk Conflicting classifications of pathogenicity TRPM6-related disorder, Inborn genetic diseases, TRPM6-related disorder
RS142946646 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS143164660 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
RS1472189003 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS147635290 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Inborn genetic diseases, Intestinal hypomagnesemia 1
RS148603803 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS148657084 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS149651828 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS150039342 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Intestinal hypomagnesemia 1, Inborn genetic diseases
RS183879985 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS191344898 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Inborn genetic diseases, Intestinal hypomagnesemia 1
RS200248159 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
RS200724937 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS201338939 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS201888532 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS2118838012 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS2489968400 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS371990882 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS372624602 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS375462836 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS542601704 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS553014740 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS553896639 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS56290308 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
RS570794624 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS570955795 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, TRPM6-related disorder, Intestinal hypomagnesemia 1
RS750071268 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS752425360 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS763977756 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS776743221 Health Risk Conflicting classifications of pathogenicity Intestinal hypomagnesemia 1, Inborn genetic diseases, Intestinal hypomagnesemia 1
RS1060499646 Health Risk Likely pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS1587550393 Health Risk Likely pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS1826688168 Health Risk Likely pathogenic
RS1828116163 Health Risk Likely pathogenic
RS2489896470 Health Risk Likely pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS2490157836 Health Risk Likely pathogenic
RS1114167360 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS1179034156 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS121912622 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS121912623 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS121912625 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS1263468898 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
RS1444779891 Health Risk Pathogenic Intestinal hypomagnesemia 1, Intestinal hypomagnesemia 1
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