THSD1 Chromosome 13

Thrombospondin type 1 domain containing 1
8 variants 8 Health Risk

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What This Gene Does
The protein encoded by this gene contains a type 1 thrombospondin domain, which is found in a number of proteins involved in the complement pathway, as well as in extracellular matrix proteins. Alternatively spliced transcript variants encoding different isoforms have been observed for this gene. [provided by RefSeq, Jan 2009]
Associated Conditions (5)
Non-immune hydrops fetalis
Lymphatic malformation 13
Aneurysm
intracranial berry
12
Key Variants
All Variants (8)
RSID Category Clinical Significance Conditions
RS141140186 Health Risk Conflicting classifications of pathogenicity
RS9536062 Health Risk Conflicting classifications of pathogenicity Non-immune hydrops fetalis, Lymphatic malformation 13, Non-immune hydrops fetalis
RS2547596958 Health Risk Likely pathogenic Lymphatic malformation 13, Lymphatic malformation 13
RS786205669 Health Risk Likely pathogenic Non-immune hydrops fetalis, Lymphatic malformation 13, Non-immune hydrops fetalis
RS1594095223 Health Risk Pathogenic Aneurysm, intracranial berry, 12
RS2547597183 Health Risk Pathogenic Lymphatic malformation 13, Lymphatic malformation 13
RS2547604512 Health Risk Pathogenic Lymphatic malformation 13, Lymphatic malformation 13
RS2547596894 Health Risk Pathogenic/Likely pathogenic
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