TAMM41 Chromosome 3

TAM41 mitochondrial translocator assembly and maintenance homolog
4 variants 4 Health Risk

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What This Gene Does
Predicted to enable phosphatidate cytidylyltransferase activity. Predicted to be involved in CDP-diacylglycerol biosynthetic process and cardiolipin biosynthetic process. Is active in mitochondrion. Implicated in combined oxidative phosphorylation deficiency 56. [provided by Alliance of Genome Resources, Jul 2025]
Associated Conditions (6)
Dysphagia
Bilateral ptosis
Gastroesophageal reflux
Respiratory failure
Combined oxidative phosphorylation deficiency 56
Acute myeloid leukemia
Key Variants
All Variants (4)
RSID Category Clinical Significance Conditions
RS2125058823 Health Risk Pathogenic Dysphagia, Bilateral ptosis, Gastroesophageal reflux
RS768826552 Health Risk Pathogenic Dysphagia, Bilateral ptosis, Gastroesophageal reflux
RS775491404 Health Risk Pathogenic Combined oxidative phosphorylation deficiency 56, Combined oxidative phosphorylation deficiency 56
RS934260435 Health Risk Pathogenic Combined oxidative phosphorylation deficiency 56, Acute myeloid leukemia, Combined oxidative phosphorylation deficiency 56
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