STAG1 Chromosome 3

STAG1 cohesin complex component
55 variants 55 Health Risk

Upload your DNA to see your personal genotypes for variants in STAG1.

What This Gene Does
This gene is a member of the SCC3 family and is expressed in the nucleus. It encodes a component of cohesin, a multisubunit protein complex that provides sister chromatid cohesion along the length of a chromosome from DNA replication through prophase and prometaphase, after which it is dissociated in preparation for segregation during anaphase. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
"Cohesin complex|Armadillo like helical domain containing|STAG family"
Locus Type
gene with protein product
Location
3q22.3
Ensembl
ENSG00000118007
Associated Conditions (9)
Inborn genetic diseases
STAG1-related disorder
Intellectual disability
autosomal dominant 47
Congenital ocular coloboma
Neurodevelopmental disorder
Neurodevelopmental delay
Global developmental delay
See cases
Key Variants
RS1026553102
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1193212374
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1268657053
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1471479119
Conflicting classifications of pathogenicity
STAG1-related disorder, Intellectual disability, autosomal dominant 47
Health Risk
RS147882530
Conflicting classifications of pathogenicity
Intellectual disability, autosomal dominant 47, Inborn genetic diseases
Health Risk
RS1939944359
Conflicting classifications of pathogenicity
Intellectual disability, autosomal dominant 47, Intellectual disability
Health Risk
RS199902670
Conflicting classifications of pathogenicity
Intellectual disability, autosomal dominant 47, STAG1-related disorder
Health Risk
RS201846240
Conflicting classifications of pathogenicity
Intellectual disability, autosomal dominant 47, Intellectual disability
Health Risk
RS2530452986
Conflicting classifications of pathogenicity
Inborn genetic diseases, Intellectual disability, autosomal dominant 47
Health Risk
RS370146152
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS748993808
Conflicting classifications of pathogenicity
Intellectual disability, autosomal dominant 47, Intellectual disability
Health Risk
RS757065909
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
All Variants (55)
RSID Category Clinical Significance Conditions
RS1026553102 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1193212374 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1268657053 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1471479119 Health Risk Conflicting classifications of pathogenicity STAG1-related disorder, Intellectual disability, autosomal dominant 47
RS147882530 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 47, Inborn genetic diseases
RS1939944359 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 47, Intellectual disability
RS199902670 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 47, STAG1-related disorder
RS201846240 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 47, Intellectual disability
RS2530452986 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Intellectual disability, autosomal dominant 47
RS370146152 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS748993808 Health Risk Conflicting classifications of pathogenicity Intellectual disability, autosomal dominant 47, Intellectual disability
RS757065909 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS758293382 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS759561079 Health Risk Conflicting classifications of pathogenicity STAG1-related disorder, Congenital ocular coloboma, STAG1-related disorder
RS768339073 Health Risk Conflicting classifications of pathogenicity
RS774492433 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS776820207 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS956934022 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1057524850 Health Risk Likely pathogenic STAG1-related disorder, STAG1-related disorder
RS1240231224 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1267304310 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1553727865 Health Risk Likely pathogenic STAG1-related disorder, STAG1-related disorder
RS1553728634 Health Risk Likely pathogenic STAG1-related disorder, STAG1-related disorder
RS1553738686 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, STAG1-related disorder
RS1553738694 Health Risk Likely pathogenic STAG1-related disorder, STAG1-related disorder
RS1553789166 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1559791842 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1560062082 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1576367919 Health Risk Likely pathogenic
RS1935927985 Health Risk Likely pathogenic
RS2107821339 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS2107821352 Health Risk Likely pathogenic Neurodevelopmental delay, Neurodevelopmental delay
RS2107831013 Health Risk Likely pathogenic Neurodevelopmental disorder, Neurodevelopmental disorder
RS2107905472 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2107905668 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2472740882 Health Risk Likely pathogenic STAG1-related disorder, STAG1-related disorder
RS2530008022 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2530021619 Health Risk Likely pathogenic
RS2530031168 Health Risk Likely pathogenic
RS2530394997 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2530398321 Health Risk Likely pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2530508103 Health Risk Likely pathogenic
RS751263539 Health Risk Likely pathogenic Global developmental delay, Global developmental delay
RS1553743217 Health Risk Pathogenic
RS1553801881 Health Risk Pathogenic
RS1576656734 Health Risk Pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS1937166346 Health Risk Pathogenic Intellectual disability, autosomal dominant 47, Intellectual disability
RS2530078152 Health Risk Pathogenic
RS2530371465 Health Risk Pathogenic
RS1376334317 Health Risk Pathogenic/Likely pathogenic Intellectual disability, autosomal dominant 47, STAG1-related disorder
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