SP7 Chromosome 12

Sp7 transcription factor
7 variants 7 Health Risk

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What This Gene Does
This gene encodes a member of the Sp subfamily of Sp/XKLF transcription factors. Sp family proteins are sequence-specific DNA-binding proteins characterized by an amino-terminal trans-activation domain and three carboxy-terminal zinc finger motifs. This protein is a bone specific transcription factor and is required for osteoblast differentiation and bone formation.[provided by RefSeq, Jul 2010]
Gene Info
Gene Group
"Zinc fingers C2H2-type|Sp transcription factors"
Locus Type
gene with protein product
Location
12q13.13
Ensembl
ENSG00000170374
Associated Conditions (2)
Osteogenesis imperfecta type 12
Osteogenesis imperfecta
Key Variants
All Variants (7)
RSID Category Clinical Significance Conditions
RS1461984773 Health Risk Conflicting classifications of pathogenicity
RS182820275 Health Risk Conflicting classifications of pathogenicity Osteogenesis imperfecta type 12, Osteogenesis imperfecta type 12
RS369792296 Health Risk Conflicting classifications of pathogenicity Osteogenesis imperfecta, Osteogenesis imperfecta
RS542641721 Health Risk Conflicting classifications of pathogenicity
RS561083858 Health Risk Conflicting classifications of pathogenicity Osteogenesis imperfecta, Osteogenesis imperfecta
RS745609349 Health Risk Likely pathogenic Osteogenesis imperfecta type 12, Osteogenesis imperfecta type 12
RS137853893 Health Risk Pathogenic Osteogenesis imperfecta type 12, Osteogenesis imperfecta type 12
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