SLC4A4 Chromosome 4

Solute carrier family 4 member 4
34 variants 34 Health Risk

Upload your DNA to see your personal genotypes for variants in SLC4A4.

What This Gene Does
This gene encodes a sodium bicarbonate cotransporter (NBC) involved in the regulation of bicarbonate secretion and absorption and intracellular pH. Mutations in this gene are associated with proximal renal tubular acidosis. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2008]
Gene Info
Gene Group
Solute carrier family 4
Locus Type
gene with protein product
Location
4q13.3
Ensembl
ENSG00000080493
Associated Conditions (11)
Autosomal recessive proximal renal tubular acidosis
SLC4A4-related disorder
Malignant tumor of urinary bladder
Inborn genetic diseases
Thyroid cancer
nonmedullary
1
Gastric cancer
Hepatocellular carcinoma
Clear cell carcinoma of kidney
Cervical cancer
Key Variants
RS1252177878
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS137982286
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS138942006
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS139191615
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Malignant tumor of urinary bladder
Health Risk
RS140882617
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Inborn genetic diseases, SLC4A4-related disorder
Health Risk
RS143924311
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS145378038
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Thyroid cancer
Health Risk
RS145739451
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS146008079
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS147651604
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS147661107
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
RS148889712
Conflicting classifications of pathogenicity
Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
Health Risk
All Variants (34)
RSID Category Clinical Significance Conditions
RS1252177878 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS137982286 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS138942006 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS139191615 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Malignant tumor of urinary bladder
RS140882617 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Inborn genetic diseases, SLC4A4-related disorder
RS143924311 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS145378038 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Thyroid cancer
RS145739451 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS146008079 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Autosomal recessive proximal renal tubular acidosis
RS147651604 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS147661107 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS148889712 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS149802590 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS181184794 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS200126485 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS200226048 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Inborn genetic diseases, Autosomal recessive proximal renal tubular acidosis
RS201092552 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS201133749 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS201149572 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS2475717504 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS35891845 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS41265669 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS550285672 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS72650362 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Gastric cancer
RS771339934 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS779558159 Health Risk Conflicting classifications of pathogenicity Autosomal recessive proximal renal tubular acidosis, SLC4A4-related disorder, Autosomal recessive proximal renal tubular acidosis
RS1725958418 Health Risk Likely pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS752089136 Health Risk Likely pathogenic SLC4A4-related disorder, SLC4A4-related disorder
RS778804628 Health Risk Likely pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS786205569 Health Risk Likely pathogenic
RS121908856 Health Risk Pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS121908857 Health Risk Pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS121908858 Health Risk Pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
RS1553913019 Health Risk Pathogenic Autosomal recessive proximal renal tubular acidosis, Autosomal recessive proximal renal tubular acidosis
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