SLC3A1 Chromosome 2

Solute carrier family 3 member 1
104 variants 104 Health Risk

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What This Gene Does
This gene encodes a type II membrane glycoprotein which is one of the components of the renal amino acid transporter which transports neutral and basic amino acids in the renal tubule and intestinal tract. Mutations and deletions in this gene are associated with cystinuria. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Solute carrier family 3
Locus Type
gene with protein product
Location
2p21
Ensembl
ENSG00000138079
Associated Conditions (9)
Cystinuria
SLC3A1-related disorder
Inborn genetic diseases
Cystine urolithiasis
See cases
Autism spectrum disorder
Kidney disorder
Nephrocalcinosis
Nephrolithiasis
Key Variants
All Variants (104)
RSID Category Clinical Significance Conditions
RS115030299 Health Risk Conflicting classifications of pathogenicity Cystinuria, SLC3A1-related disorder, Cystinuria
RS139310305 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS140317484 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS140821819 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS1408497251 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Cystinuria, Inborn genetic diseases
RS141587158 Health Risk Conflicting classifications of pathogenicity Cystinuria, SLC3A1-related disorder, Cystinuria
RS141944551 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS143068960 Health Risk Conflicting classifications of pathogenicity Cystinuria, SLC3A1-related disorder, Cystinuria
RS144065614 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS144162964 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS146630359 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS146963107 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS1484579709 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS148703534 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS149507807 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS150557210 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS150870922 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS200592320 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS201617723 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS2466682288 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS370262167 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS371537299 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS373852467 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS375399468 Health Risk Conflicting classifications of pathogenicity Cystine urolithiasis, Cystine urolithiasis, Cystinuria
RS555017366 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS557669708 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS698761 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS755742518 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS760943092 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS763292534 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS768848958 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS770801300 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS771021431 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS778276427 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS886056069 Health Risk Conflicting classifications of pathogenicity Cystinuria, Cystinuria
RS1206425661 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS121912693 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS1249821286 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS1558450604 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS1558455633 Health Risk Likely pathogenic
RS1558455640 Health Risk Likely pathogenic
RS1572804699 Health Risk Likely pathogenic Cystine urolithiasis, Cystine urolithiasis
RS1671960904 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS1672093819 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS200001778 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS2104342335 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS2104364101 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS2465902056 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS2465939469 Health Risk Likely pathogenic Cystinuria, Cystinuria
RS2465949850 Health Risk Likely pathogenic Cystinuria, Cystinuria
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