SLC34A1 Chromosome 5

Solute carrier family 34 member 1
67 variants 67 Health Risk

Upload your DNA to see your personal genotypes for variants in SLC34A1.

What This Gene Does
Enables sodium:phosphate symporter activity. Involved in several processes, including phosphate ion homeostasis; response to cadmium ion; and response to lead ion. Located in several cellular components, including apical plasma membrane; mitotic spindle; and nuclear speck. Implicated in several diseases, including Fanconi syndrome (multiple); chronic kidney disease; hereditary hypophosphatemic rickets with hypercalciuria; hypophosphatemic nephrolithiasis/osteoporosis 1; and nephrolithiasis. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Solute carrier family 34
Locus Type
gene with protein product
Location
5q35.3
Ensembl
ENSG00000131183
Associated Conditions (12)
Hypophosphatemic nephrolithiasis/osteoporosis 1
Fanconi renotubular syndrome 2
Hypercalcemia
infantile
2
SLC34A1-related disorder
Inborn genetic diseases
Nephrocalcinosis
Nephrolithiasis
Gastric cancer
Osteogenesis imperfecta type III
Autosomal recessive infantile hypercalcemia
Key Variants
RS112528230
Conflicting classifications of pathogenicity
Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
Health Risk
RS1163121743
Conflicting classifications of pathogenicity
Fanconi renotubular syndrome 2, Hypercalcemia, infantile
Health Risk
RS1306742152
Conflicting classifications of pathogenicity
SLC34A1-related disorder, SLC34A1-related disorder
Health Risk
RS140649226
Conflicting classifications of pathogenicity
Hypercalcemia, infantile, 2
Health Risk
RS143201338
Conflicting classifications of pathogenicity
Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
Health Risk
RS144306414
Conflicting classifications of pathogenicity
Hypophosphatemic nephrolithiasis/osteoporosis 1, SLC34A1-related disorder, Hypercalcemia
Health Risk
RS146919762
Conflicting classifications of pathogenicity
Hypercalcemia, infantile, 2
Health Risk
RS148615663
Conflicting classifications of pathogenicity
Fanconi renotubular syndrome 2, Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia
Health Risk
RS148669433
Conflicting classifications of pathogenicity
Hypophosphatemic nephrolithiasis/osteoporosis 1, Inborn genetic diseases, Hypercalcemia
Health Risk
RS148976897
Conflicting classifications of pathogenicity
Hypophosphatemic nephrolithiasis/osteoporosis 1, Nephrocalcinosis, Hypercalcemia
Health Risk
RS1554095263
Conflicting classifications of pathogenicity
Fanconi renotubular syndrome 2, Hypercalcemia, infantile
Health Risk
RS1762582225
Conflicting classifications of pathogenicity
Hypercalcemia, infantile, 2
Health Risk
All Variants (67)
RSID Category Clinical Significance Conditions
RS112528230 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS1163121743 Health Risk Conflicting classifications of pathogenicity Fanconi renotubular syndrome 2, Hypercalcemia, infantile
RS1306742152 Health Risk Conflicting classifications of pathogenicity SLC34A1-related disorder, SLC34A1-related disorder
RS140649226 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS143201338 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
RS144306414 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, SLC34A1-related disorder, Hypercalcemia
RS146919762 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS148615663 Health Risk Conflicting classifications of pathogenicity Fanconi renotubular syndrome 2, Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia
RS148669433 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Inborn genetic diseases, Hypercalcemia
RS148976897 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Nephrocalcinosis, Hypercalcemia
RS1554095263 Health Risk Conflicting classifications of pathogenicity Fanconi renotubular syndrome 2, Hypercalcemia, infantile
RS1762582225 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS1763019193 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS199565633 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
RS201331677 Health Risk Conflicting classifications of pathogenicity Nephrolithiasis, Nephrocalcinosis, SLC34A1-related disorder
RS202081023 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
RS2127355139 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS34044544 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Fanconi renotubular syndrome 2, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS369770760 Health Risk Conflicting classifications of pathogenicity
RS372577906 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Fanconi renotubular syndrome 2, Hypercalcemia
RS372860328 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS376448083 Health Risk Conflicting classifications of pathogenicity
RS377186926 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS548223568 Health Risk Conflicting classifications of pathogenicity Fanconi renotubular syndrome 2, Fanconi renotubular syndrome 2
RS548844573 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Fanconi renotubular syndrome 2, Hypercalcemia
RS561557630 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS570463028 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS753845247 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS754825865 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS756685605 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
RS763096294 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Inborn genetic diseases, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS765766600 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Hypercalcemia, infantile
RS773115741 Health Risk Conflicting classifications of pathogenicity Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS777574121 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Fanconi renotubular syndrome 2, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS777694025 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS876661296 Health Risk Conflicting classifications of pathogenicity Hypercalcemia, infantile, 2
RS1185100306 Health Risk Likely pathogenic
RS1298448088 Health Risk Likely pathogenic SLC34A1-related disorder, SLC34A1-related disorder
RS1364012682 Health Risk Likely pathogenic
RS141827822 Health Risk Likely pathogenic
RS1554095500 Health Risk Likely pathogenic Hypercalcemia, infantile, 2
RS1581634382 Health Risk Likely pathogenic Osteogenesis imperfecta type III, Osteogenesis imperfecta type III
RS188409125 Health Risk Likely pathogenic Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypercalcemia, infantile
RS2481008620 Health Risk Likely pathogenic Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS765036417 Health Risk Likely pathogenic
RS765915351 Health Risk Likely pathogenic
RS770557903 Health Risk Likely pathogenic Fanconi renotubular syndrome 2, Fanconi renotubular syndrome 2
RS1174958403 Health Risk Pathogenic Hypercalcemia, infantile, 2
RS121918610 Health Risk Pathogenic Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
RS1272063335 Health Risk Pathogenic Hypophosphatemic nephrolithiasis/osteoporosis 1, Hypophosphatemic nephrolithiasis/osteoporosis 1
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