SI Chromosome 3
Sucrase-isomaltase
Upload your DNA to see your personal genotypes for variants in SI.
What This Gene Does
This gene encodes a sucrase-isomaltase enzyme that is expressed in the intestinal brush border. The encoded protein is synthesized as a precursor protein that is cleaved by pancreatic proteases into two enzymatic subunits sucrase and isomaltase. These two subunits heterodimerize to form the sucrose-isomaltase complex. This complex is essential for the digestion of dietary carbohydrates including starch, sucrose and isomaltose. Mutations in this gene are the cause of congenital sucrase-isomaltase deficiency.[provided by RefSeq, Apr 2010]
Gene Info
Gene Group
Glycoside hydrolase family 31
Locus Type
gene with protein product
Location
3q26.1
Ensembl
ENSG00000090402
Associated Conditions (5)
Inborn genetic diseases
Sucrase-isomaltase deficiency
SI-related disorder
Malignant tumor of urinary bladder
Congenital sucrose-isomaltase deficiency
Key Variants
RS111316957
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS112259253
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS113826825
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS115295826
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS121912615
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency
Health Risk
RS121912616
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Inborn genetic diseases, SI-related disorder
Health Risk
RS138374817
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Inborn genetic diseases, Sucrase-isomaltase deficiency
Health Risk
RS138434001
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS138564183
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS139504152
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS139867598
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
RS139876383
Conflicting classifications of pathogenicity
Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency
Health Risk
All Variants (189)
| RSID | Category | Clinical Significance | Conditions |
|---|---|---|---|
| RS111316957 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS112259253 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS113826825 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS115295826 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS121912615 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS121912616 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Inborn genetic diseases, SI-related disorder |
| RS138374817 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Inborn genetic diseases, Sucrase-isomaltase deficiency |
| RS138434001 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS138564183 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS139504152 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS139867598 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS139876383 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS139908762 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, SI-related disorder, Inborn genetic diseases |
| RS140287192 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS142090504 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS142205728 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS142447888 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS142838612 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS142838806 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS143388292 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS144206255 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS1444268809 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS144579834 | Health Risk | Conflicting classifications of pathogenicity | SI-related disorder, Inborn genetic diseases, SI-related disorder |
| RS144972103 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS1453717899 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS145486890 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS145556619 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS145891116 | Health Risk | Conflicting classifications of pathogenicity | SI-related disorder, Inborn genetic diseases, SI-related disorder |
| RS145893756 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS146222650 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS146501096 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS146539849 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS146785675 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS146830505 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Inborn genetic diseases, Sucrase-isomaltase deficiency |
| RS146899814 | Health Risk | Conflicting classifications of pathogenicity | SI-related disorder, Inborn genetic diseases, SI-related disorder |
| RS147207752 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS147226975 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS1487909793 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS148831941 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS149783130 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS150131334 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS150246328 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, SI-related disorder, Sucrase-isomaltase deficiency |
| RS150428844 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS150702232 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS150927256 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS1718540793 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS1718837805 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS185479515 | Health Risk | Conflicting classifications of pathogenicity | Inborn genetic diseases, Inborn genetic diseases |
| RS199581970 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |
| RS200646132 | Health Risk | Conflicting classifications of pathogenicity | Sucrase-isomaltase deficiency, Sucrase-isomaltase deficiency |