SH2B1 Chromosome 16

SH2B adaptor protein 1
8 variants 8 Health Risk

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What This Gene Does
This gene encodes a member of the SH2-domain containing mediators family. The encoded protein mediates activation of various kinases and may function in cytokine and growth factor receptor signaling and cellular transformation. Alternatively spliced transcript variants have been described. [provided by RefSeq, Mar 2009]
Gene Info
Gene Group
"Pleckstrin homology domain containing|SH2 domain containing"
Locus Type
gene with protein product
Location
16p11.2
Ensembl
ENSG00000178188
Associated Conditions (5)
SH2B1-related disorder
Premature ovarian failure
Distal 16p11.2 microdeletion syndrome
Severe early-onset obesity-insulin resistance syndrome due to SH2B1 deficiency
Lung cancer
Key Variants
All Variants (8)
RSID Category Clinical Significance Conditions
RS1050082155 Health Risk Conflicting classifications of pathogenicity SH2B1-related disorder, SH2B1-related disorder
RS115698674 Health Risk Conflicting classifications of pathogenicity SH2B1-related disorder, SH2B1-related disorder
RS142515048 Health Risk Conflicting classifications of pathogenicity Premature ovarian failure, Distal 16p11.2 microdeletion syndrome, SH2B1-related disorder
RS144126859 Health Risk Conflicting classifications of pathogenicity
RS149091795 Health Risk Conflicting classifications of pathogenicity SH2B1-related disorder, SH2B1-related disorder
RS2152178267 Health Risk Conflicting classifications of pathogenicity Severe early-onset obesity-insulin resistance syndrome due to SH2B1 deficiency, Severe early-onset obesity-insulin resistance syndrome due to SH2B1 deficiency
RS367969323 Health Risk Conflicting classifications of pathogenicity Lung cancer, Lung cancer
RS769421511 Health Risk Conflicting classifications of pathogenicity
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