SERPINA6 Chromosome 14

Serpin family A member 6
4 variants 4 Health Risk

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What This Gene Does
This gene encodes an alpha-globulin protein with corticosteroid-binding properties. This is the major transport protein for glucorticoids and progestins in the blood of most vertebrates. The gene localizes to a chromosomal region containing several closely related serine protease inhibitors which may have evolved by duplication events. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Serpin peptidase inhibitors
Locus Type
gene with protein product
Location
14q32.13
Ensembl
ENSG00000170099
Associated Conditions (2)
Corticosteroid-binding globulin deficiency
SERPINA6-related disorder
Key Variants
All Variants (4)
RSID Category Clinical Significance Conditions
RS113418909 Health Risk Conflicting classifications of pathogenicity Corticosteroid-binding globulin deficiency, SERPINA6-related disorder, Corticosteroid-binding globulin deficiency
RS28929488 Health Risk Conflicting classifications of pathogenicity Corticosteroid-binding globulin deficiency, SERPINA6-related disorder, Corticosteroid-binding globulin deficiency
RS771441863 Health Risk Likely pathogenic Corticosteroid-binding globulin deficiency, Corticosteroid-binding globulin deficiency
RS777245398 Health Risk Pathogenic Corticosteroid-binding globulin deficiency, Corticosteroid-binding globulin deficiency
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