RTN2 Chromosome 19

Reticulon 2
34 variants 34 Health Risk

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What This Gene Does
This gene belongs to the family of reticulon encoding genes. Reticulons are associated with the endoplasmic reticulum, and are involved in neuroendocrine secretion or in membrane trafficking in neuroendocrine cells. Reticulon proteins also play an important role in the replication of positive-strand RNA (ssRNA) viruses. Mutations at this locus have been associated with autosomal dominant spastic paraplegia-12. [provided by RefSeq, Aug 2020]
Gene Info
Gene Group
Reticulons
Locus Type
gene with protein product
Location
19q13.32
Ensembl
ENSG00000125744
Associated Conditions (12)
Spastic paraplegia
Inborn genetic diseases
Hereditary spastic paraplegia 12
Hereditary spastic paraplegia
RTN2-related disorder
Thyroid cancer
nonmedullary
1
Neuronopathy
distal hereditary motor
autosomal recessive 11
with spasticity
Key Variants
RS1176639498
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
Health Risk
RS138317158
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
Health Risk
RS1440427338
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS145653668
Conflicting classifications of pathogenicity
Hereditary spastic paraplegia 12, Spastic paraplegia, Inborn genetic diseases
Health Risk
RS1568624823
Conflicting classifications of pathogenicity
Hereditary spastic paraplegia 12, Hereditary spastic paraplegia 12
Health Risk
RS201387324
Conflicting classifications of pathogenicity
Spastic paraplegia, Hereditary spastic paraplegia 12, Inborn genetic diseases
Health Risk
RS201863499
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
Health Risk
RS2513743882
Conflicting classifications of pathogenicity
Hereditary spastic paraplegia 12, Hereditary spastic paraplegia 12
Health Risk
RS3038807
Conflicting classifications of pathogenicity
Hereditary spastic paraplegia, Hereditary spastic paraplegia, Hereditary spastic paraplegia
Health Risk
RS369158895
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, Hereditary spastic paraplegia
Health Risk
RS374003662
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
Health Risk
RS532500975
Conflicting classifications of pathogenicity
Spastic paraplegia, Inborn genetic diseases, RTN2-related disorder
Health Risk
All Variants (34)
RSID Category Clinical Significance Conditions
RS1176639498 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
RS138317158 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
RS1440427338 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS145653668 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia 12, Spastic paraplegia, Inborn genetic diseases
RS1568624823 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia 12, Hereditary spastic paraplegia 12
RS201387324 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Hereditary spastic paraplegia 12, Inborn genetic diseases
RS201863499 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
RS2513743882 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia 12, Hereditary spastic paraplegia 12
RS3038807 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia, Hereditary spastic paraplegia, Hereditary spastic paraplegia
RS369158895 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Hereditary spastic paraplegia
RS374003662 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
RS532500975 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, RTN2-related disorder
RS561232438 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Inborn genetic diseases, Spastic paraplegia
RS745409162 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Spastic paraplegia
RS748397131 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia 12, Spastic paraplegia, Hereditary spastic paraplegia 12
RS748824542 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Hereditary spastic paraplegia, Spastic paraplegia
RS749104931 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Spastic paraplegia
RS761286207 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, Spastic paraplegia
RS767066842 Health Risk Conflicting classifications of pathogenicity Spastic paraplegia, RTN2-related disorder, Inborn genetic diseases
RS768449676 Health Risk Conflicting classifications of pathogenicity Hereditary spastic paraplegia 12, Spastic paraplegia, Hereditary spastic paraplegia 12
RS1421302939 Health Risk Likely pathogenic Thyroid cancer, nonmedullary, 1
RS1568625691 Health Risk Likely pathogenic
RS1599914870 Health Risk Likely pathogenic
RS1968087179 Health Risk Likely pathogenic Spastic paraplegia, Spastic paraplegia
RS2513733818 Health Risk Likely pathogenic
RS1968243327 Health Risk Pathogenic Hereditary spastic paraplegia 12, Hereditary spastic paraplegia 12
RS2513742001 Health Risk Pathogenic Neuronopathy, distal hereditary motor, autosomal recessive 11
RS2513743643 Health Risk Pathogenic Neuronopathy, distal hereditary motor, autosomal recessive 11
RS561968273 Health Risk Pathogenic Neuronopathy, distal hereditary motor, autosomal recessive 11
RS758370815 Health Risk Pathogenic Spastic paraplegia, Spastic paraplegia
RS763387041 Health Risk Pathogenic Hereditary spastic paraplegia 12, Neuronopathy, distal hereditary motor
RS1162797495 Health Risk Pathogenic/Likely pathogenic Spastic paraplegia, Hereditary spastic paraplegia 12, Spastic paraplegia
RS1968241252 Health Risk Pathogenic/Likely pathogenic Spastic paraplegia, Hereditary spastic paraplegia 12, Spastic paraplegia
RS2513740146 Health Risk Pathogenic/Likely pathogenic Hereditary spastic paraplegia 12, Spastic paraplegia, Hereditary spastic paraplegia 12
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