RFWD3 Chromosome 16

Ring finger and WD repeat domain 3
13 variants 13 Health Risk

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What This Gene Does
Enables MDM2/MDM4 family protein binding activity; p53 binding activity; and ubiquitin protein ligase activity. Involved in several processes, including DNA metabolic process; regulation of cell cycle phase transition; and response to ionizing radiation. Located in nucleoplasm and site of double-strand break. Implicated in Fanconi anemia complementation group W. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
"Ring finger proteins|WD repeat domain containing|FA complementation groups"
Locus Type
gene with protein product
Location
16q23.1
Ensembl
ENSG00000168411
Associated Conditions (3)
RFWD3-related disorder
Fanconi anemia
complementation group W
Key Variants
All Variants (13)
RSID Category Clinical Significance Conditions
RS1030253516 Health Risk Conflicting classifications of pathogenicity
RS141685768 Health Risk Conflicting classifications of pathogenicity
RS1433703349 Health Risk Conflicting classifications of pathogenicity
RS148545931 Health Risk Conflicting classifications of pathogenicity RFWD3-related disorder, RFWD3-related disorder
RS549212476 Health Risk Conflicting classifications of pathogenicity RFWD3-related disorder, RFWD3-related disorder
RS755700844 Health Risk Conflicting classifications of pathogenicity
RS766228902 Health Risk Conflicting classifications of pathogenicity
RS768967844 Health Risk Conflicting classifications of pathogenicity
RS775043994 Health Risk Conflicting classifications of pathogenicity
RS777224972 Health Risk Conflicting classifications of pathogenicity
RS977485902 Health Risk Conflicting classifications of pathogenicity
RS1555524842 Health Risk Pathogenic Fanconi anemia, complementation group W, Fanconi anemia
RS1961408684 Health Risk Pathogenic
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