RELA Chromosome 11

RELA proto-oncogene, NF-kB subunit
32 variants 32 Health Risk

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What This Gene Does
NF-kappa-B is a ubiquitous transcription factor involved in several biological processes. It is held in the cytoplasm in an inactive state by specific inhibitors. Upon degradation of the inhibitor, NF-kappa-B moves to the nucleus and activates transcription of specific genes. NF-kappa-B is composed of NFKB1 or NFKB2 bound to either REL, RELA, or RELB. The most abundant form of NF-kappa-B is NFKB1 complexed with the product of this gene, RELA. Four transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Sep 2011]
Gene Info
Gene Group
"NF-kappa B complex subunits|IPT domain containing"
Locus Type
gene with protein product
Location
11q13.1
Ensembl
ENSG00000173039
Associated Conditions (4)
Mucocutaneous ulceration
chronic
RELA-related disorder
Childhood-onset schizophrenia
Key Variants
All Variants (32)
RSID Category Clinical Significance Conditions
RS1190765527 Health Risk Conflicting classifications of pathogenicity Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS145138143 Health Risk Conflicting classifications of pathogenicity Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS199846198 Health Risk Conflicting classifications of pathogenicity
RS201037601 Health Risk Conflicting classifications of pathogenicity
RS763729954 Health Risk Conflicting classifications of pathogenicity Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS1590931704 Health Risk Likely pathogenic Mucocutaneous ulceration, Mucocutaneous ulceration
RS2496867941 Health Risk Likely pathogenic RELA-related disorder, RELA-related disorder
RS2496871237 Health Risk Likely pathogenic
RS749716796 Health Risk Likely pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS863223356 Health Risk Likely pathogenic Childhood-onset schizophrenia, Childhood-onset schizophrenia
RS1213368057 Health Risk Pathogenic
RS1268667021 Health Risk Pathogenic
RS149145548 Health Risk Pathogenic Mucocutaneous ulceration, chronic, RELA-related disorder
RS1565190345 Health Risk Pathogenic
RS1565191003 Health Risk Pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS1590937041 Health Risk Pathogenic
RS2135548845 Health Risk Pathogenic
RS2135549951 Health Risk Pathogenic
RS2135572911 Health Risk Pathogenic
RS2496824516 Health Risk Pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS2496825673 Health Risk Pathogenic
RS2496826579 Health Risk Pathogenic
RS2496827042 Health Risk Pathogenic
RS2496833014 Health Risk Pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS2496834411 Health Risk Pathogenic
RS2496847338 Health Risk Pathogenic
RS2496848830 Health Risk Pathogenic
RS2496858372 Health Risk Pathogenic
RS929817187 Health Risk Pathogenic
RS1326268854 Health Risk Pathogenic/Likely pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
RS1856484601 Health Risk Pathogenic/Likely pathogenic RELA-related disorder, RELA-related disorder
RS2496827835 Health Risk Pathogenic/Likely pathogenic Mucocutaneous ulceration, chronic, Mucocutaneous ulceration
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