RDH11 Chromosome 14

Retinol dehydrogenase 11
6 variants 6 Health Risk

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What This Gene Does
Enables all-trans-retinol dehydrogenase (NADP+) activity. Involved in cellular detoxification of aldehyde and retinoid metabolic process. Acts upstream of or within retinal metabolic process. Located in endoplasmic reticulum membrane. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Short chain dehydrogenase/reductase superfamily
Locus Type
gene with protein product
Location
14q24.1
Ensembl
ENSG00000072042
Associated Conditions (1)
Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome
Key Variants
All Variants (6)
RSID Category Clinical Significance Conditions
RS1470605735 Health Risk Likely pathogenic Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome, Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome
RS1017775999 Health Risk Pathogenic
RS1176694083 Health Risk Pathogenic
RS2140082978 Health Risk Pathogenic
RS606231423 Health Risk Pathogenic Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome, Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome
RS606231424 Health Risk Pathogenic Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome, Retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome
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