PPP1CB Chromosome 2

Protein phosphatase 1 catalytic subunit beta
16 variants 16 Health Risk

Upload your DNA to see your personal genotypes for variants in PPP1CB.

What This Gene Does
The protein encoded by this gene is one of the three catalytic subunits of protein phosphatase 1 (PP1). PP1 is a serine/threonine specific protein phosphatase known to be involved in the regulation of a variety of cellular processes, such as cell division, glycogen metabolism, muscle contractility, protein synthesis, and HIV-1 viral transcription. Mouse studies suggest that PP1 functions as a suppressor of learning and memory. Two alternatively spliced transcript variants encoding distinct isoforms have been observed. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Protein phosphatase catalytic subunits
Locus Type
gene with protein product
Location
2p23.2
Ensembl
ENSG00000213639
Associated Conditions (9)
Cardiovascular phenotype
PPP1CB-related disorder
Noonan syndrome
Noonan syndrome-like disorder with loose anagen hair 2
RASopathy
Dandy-Walker syndrome
Inborn genetic diseases
Neurodevelopmental delay
Noonan syndrome-like disorder with loose anagen hair
Key Variants
All Variants (16)
RSID Category Clinical Significance Conditions
RS1667056053 Health Risk Conflicting classifications of pathogenicity
RS201449923 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Cardiovascular phenotype
RS202171795 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, PPP1CB-related disorder, Cardiovascular phenotype
RS2465745645 Health Risk Conflicting classifications of pathogenicity
RS747468547 Health Risk Conflicting classifications of pathogenicity PPP1CB-related disorder, PPP1CB-related disorder
RS768286092 Health Risk Conflicting classifications of pathogenicity Noonan syndrome, Noonan syndrome
RS1114167429 Health Risk Likely pathogenic Noonan syndrome-like disorder with loose anagen hair 2, RASopathy, Noonan syndrome-like disorder with loose anagen hair 2
RS1553310744 Health Risk Likely pathogenic
RS2465732793 Health Risk Likely pathogenic Noonan syndrome-like disorder with loose anagen hair 2, Noonan syndrome-like disorder with loose anagen hair 2
RS2465753864 Health Risk Likely pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS886037953 Health Risk Likely pathogenic
RS886037955 Health Risk Likely pathogenic Noonan syndrome-like disorder with loose anagen hair 2, PPP1CB-related disorder, RASopathy
RS886037952 Health Risk Pathogenic Noonan syndrome-like disorder with loose anagen hair 2, Noonan syndrome, Dandy-Walker syndrome
RS886037954 Health Risk Pathogenic Noonan syndrome-like disorder with loose anagen hair 2, RASopathy, Cardiovascular phenotype
RS1553311527 Health Risk Pathogenic/Likely pathogenic Noonan syndrome-like disorder with loose anagen hair 2, Noonan syndrome-like disorder with loose anagen hair 2
RS2465736021 Health Risk Pathogenic/Likely pathogenic Noonan syndrome, Noonan syndrome-like disorder with loose anagen hair 2, Noonan syndrome
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