PKDCC Chromosome 2

Protein kinase domain containing, cytoplasmic
18 variants 18 Health Risk

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What This Gene Does
Enables non-membrane spanning protein tyrosine kinase activity. Involved in peptidyl-tyrosine phosphorylation and skeletal system development. Located in extracellular region. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Divergent protein kinase domain family
Locus Type
gene with protein product
Location
2p21
Ensembl
ENSG00000162878
Associated Conditions (5)
Inborn genetic diseases
PKDCC-related disorder
Skeletal dysplasia
Rhizomelic limb shortening with dysmorphic features
Abnormality of the skeletal system
Key Variants
All Variants (18)
RSID Category Clinical Significance Conditions
RS1325693451 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS534596867 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, PKDCC-related disorder, Skeletal dysplasia
RS61754921 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, PKDCC-related disorder, Inborn genetic diseases
RS751205624 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1667907522 Health Risk Likely pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS2103930689 Health Risk Likely pathogenic
RS2465740345 Health Risk Likely pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS369267445 Health Risk Likely pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS1408935815 Health Risk Pathogenic
RS2465376540 Health Risk Pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS2465740348 Health Risk Pathogenic
RS2465741354 Health Risk Pathogenic
RS2465741582 Health Risk Pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS761532715 Health Risk Pathogenic Inborn genetic diseases, Rhizomelic limb shortening with dysmorphic features, Inborn genetic diseases
RS776527541 Health Risk Pathogenic
RS1158542233 Health Risk Pathogenic/Likely pathogenic Rhizomelic limb shortening with dysmorphic features, Rhizomelic limb shortening with dysmorphic features
RS373676533 Health Risk Pathogenic/Likely pathogenic Abnormality of the skeletal system, Rhizomelic limb shortening with dysmorphic features, Abnormality of the skeletal system
RS763243200 Health Risk Pathogenic/Likely pathogenic Inborn genetic diseases, Rhizomelic limb shortening with dysmorphic features, Inborn genetic diseases
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