NFKB2 Chromosome 10

Nuclear factor kappa B subunit 2
28 variants 28 Health Risk

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What This Gene Does
This gene encodes a subunit of the transcription factor complex nuclear factor-kappa-B (NFkB). The NFkB complex is expressed in numerous cell types and functions as a central activator of genes involved in inflammation and immune function. The protein encoded by this gene can function as both a transcriptional activator or repressor depending on its dimerization partner. The p100 full-length protein is co-translationally processed into a p52 active form. Chromosomal rearrangements and translocations of this locus have been observed in B cell lymphomas, some of which may result in the formation of fusion proteins. There is a pseudogene for this gene on chromosome 18. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Dec 2013]
Gene Info
Gene Group
"Ankyrin repeat domain containing|NF-kappa B complex subunits|IPT domain containing"
Locus Type
gene with protein product
Location
10q24.32
Ensembl
ENSG00000077150
Associated Conditions (14)
Immunodeficiency
common variable
10
Inborn genetic diseases
NFKB2-related disorder
Colon adenocarcinoma
Uterine carcinosarcoma
Cervical cancer
Familial cancer of breast
Sarcoma
Malignant tumor of esophagus
Uveal melanoma
Inherited Immunodeficiency Diseases
1
Key Variants
All Variants (28)
RSID Category Clinical Significance Conditions
RS1182148645 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS1274576794 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS1350425608 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS1565205722 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS200227171 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS201550645 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS202001697 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS2135437164 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS367889547 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS374942288 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS563687760 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS727502788 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS777839462 Health Risk Conflicting classifications of pathogenicity Immunodeficiency, common variable, 10
RS1064795232 Health Risk Likely pathogenic
RS1565214594 Health Risk Likely pathogenic Immunodeficiency, common variable, 10
RS2061116343 Health Risk Likely pathogenic Immunodeficiency, common variable, 10
RS2061278560 Health Risk Likely pathogenic Immunodeficiency, common variable, 10
RS2544591393 Health Risk Likely pathogenic Immunodeficiency, common variable, 10
RS747113965 Health Risk Likely pathogenic NFKB2-related disorder, NFKB2-related disorder
RS1565207233 Health Risk Pathogenic
RS1565214993 Health Risk Pathogenic Immunodeficiency, common variable, 10
RS1589866171 Health Risk Pathogenic Inherited Immunodeficiency Diseases, Inherited Immunodeficiency Diseases
RS2061279365 Health Risk Pathogenic Immunodeficiency, common variable, 10
RS2135443636 Health Risk Pathogenic Immunodeficiency, common variable, 10
RS397514331 Health Risk Pathogenic Immunodeficiency, common variable, 1
RS727502786 Health Risk Pathogenic Immunodeficiency, common variable, 10
RS748910652 Health Risk Pathogenic Inherited Immunodeficiency Diseases, Inherited Immunodeficiency Diseases
RS727502787 Health Risk Pathogenic/Likely pathogenic Immunodeficiency, common variable, 10
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