NFIB Chromosome 9

Nuclear factor I B
30 variants 30 Health Risk

Upload your DNA to see your personal genotypes for variants in NFIB.

What This Gene Does
Enables DNA-binding transcription activator activity, RNA polymerase II-specific; RNA polymerase II cis-regulatory region sequence-specific DNA binding activity; and transcription regulator inhibitor activity. Involved in brain development and regulation of DNA-templated transcription. Located in fibrillar center and nucleoplasm. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Nuclear factor I family
Locus Type
gene with protein product
Location
9p23-p22.3
Ensembl
ENSG00000147862
Associated Conditions (7)
Macrocephaly
acquired
with impaired intellectual development
Inborn genetic diseases
See cases
Intellectual disability
Marfanoid habitus and intellectual disability
Key Variants
All Variants (30)
RSID Category Clinical Significance Conditions
RS2060062099 Health Risk Conflicting classifications of pathogenicity Macrocephaly, acquired, with impaired intellectual development
RS753551959 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1011357372 Health Risk Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS1587053767 Health Risk Likely pathogenic
RS2060074543 Health Risk Likely pathogenic
RS2132702648 Health Risk Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2132704027 Health Risk Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2537830164 Health Risk Likely pathogenic Inborn genetic diseases, Inborn genetic diseases
RS2537886940 Health Risk Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2538992151 Health Risk Likely pathogenic See cases, See cases
RS2538992242 Health Risk Likely pathogenic
RS2538992538 Health Risk Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS1268417773 Health Risk Pathogenic
RS1554639173 Health Risk Pathogenic Macrocephaly, Intellectual disability, acquired
RS1554649366 Health Risk Pathogenic Macrocephaly, Intellectual disability, acquired
RS1554709683 Health Risk Pathogenic Macrocephaly, Intellectual disability, acquired
RS1554709792 Health Risk Pathogenic Intellectual disability, Macrocephaly, acquired
RS2537829946 Health Risk Pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2538098365 Health Risk Pathogenic
RS2538135168 Health Risk Pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2538994311 Health Risk Pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2539031078 Health Risk Pathogenic Macrocephaly, acquired, with impaired intellectual development
RS966707448 Health Risk Pathogenic
RS1364033144 Health Risk Pathogenic/Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS1554709654 Health Risk Pathogenic/Likely pathogenic Macrocephaly, Intellectual disability, acquired
RS1554709662 Health Risk Pathogenic/Likely pathogenic Macrocephaly, Intellectual disability, acquired
RS1588253471 Health Risk Pathogenic/Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2132702633 Health Risk Pathogenic/Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS2132704082 Health Risk Pathogenic/Likely pathogenic Macrocephaly, acquired, with impaired intellectual development
RS764333096 Health Risk Pathogenic/Likely pathogenic Intellectual disability, Macrocephaly, acquired
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