NCAPD3 Chromosome 11

Non-SMC condensin II complex subunit D3
10 variants 10 Health Risk

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What This Gene Does
Condensin complexes I and II play essential roles in mitotic chromosome assembly and segregation. Both condensins contain 2 invariant structural maintenance of chromosome (SMC) subunits, SMC2 (MIM 605576) and SMC4 (MIM 605575), but they contain different sets of non-SMC subunits. NCAPD3 is 1 of 3 non-SMC subunits that define condensin II (Ono et al., 2003 [PubMed 14532007]).[supplied by OMIM, Mar 2008]
Gene Info
Gene Group
"Condensin II subunits|Armadillo like helical domain containing"
Locus Type
gene with protein product
Location
11q25
Ensembl
ENSG00000151503
Associated Conditions (5)
Microcephaly 22
primary
autosomal recessive
Intellectual disability
See cases
Key Variants
All Variants (10)
RSID Category Clinical Significance Conditions
RS138551616 Health Risk Conflicting classifications of pathogenicity Microcephaly 22, primary, autosomal recessive
RS141965615 Health Risk Conflicting classifications of pathogenicity Intellectual disability, Intellectual disability
RS143833204 Health Risk Conflicting classifications of pathogenicity Microcephaly 22, primary, autosomal recessive
RS1164631127 Health Risk Likely pathogenic Microcephaly 22, primary, autosomal recessive
RS1944165127 Health Risk Likely pathogenic See cases, See cases
RS2497410235 Health Risk Likely pathogenic Microcephaly 22, primary, autosomal recessive
RS1350194762 Health Risk Pathogenic Microcephaly 22, primary, autosomal recessive
RS1555139372 Health Risk Pathogenic Microcephaly 22, primary, autosomal recessive
RS1555143325 Health Risk Pathogenic Microcephaly 22, primary, autosomal recessive
RS773824610 Health Risk Pathogenic Microcephaly 22, primary, autosomal recessive
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