NBEAL2 Chromosome 3

Neurobeachin like 2
94 variants 94 Health Risk

Upload your DNA to see your personal genotypes for variants in NBEAL2.

What This Gene Does
The protein encoded by this gene contains a beige and Chediak-Higashi (BEACH) domain and multiple WD40 domains, and may play a role in megakaryocyte alpha-granule biogenesis. Mutations in this gene are a cause of gray platelet syndrome. [provided by RefSeq, Dec 2011]
Gene Info
Gene Group
"WD repeat domain containing|BEACH domain containing |Armadillo like helical domain containing"
Locus Type
gene with protein product
Location
3p21.31
Ensembl
ENSG00000160796
Associated Conditions (14)
Gray platelet syndrome
Thrombocytopenia
Abnormal bleeding
Inborn genetic diseases
NBEAL2-related disorder
Colon adenocarcinoma
Ovarian serous cystadenocarcinoma
Uveal melanoma
Sarcoma
Acute myeloid leukemia
Malignant tumor of esophagus
Ovarian cancer
Malignant tumor of urinary bladder
Pancreatic adenocarcinoma
Key Variants
RS140354422
Conflicting classifications of pathogenicity
Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
Health Risk
RS144664865
Conflicting classifications of pathogenicity
Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
Health Risk
RS145760682
Conflicting classifications of pathogenicity
Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
Health Risk
RS181413143
Conflicting classifications of pathogenicity
Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
Health Risk
RS185057557
Conflicting classifications of pathogenicity
Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
Health Risk
RS187699322
Conflicting classifications of pathogenicity
Health Risk
RS199797249
Conflicting classifications of pathogenicity
Gray platelet syndrome, Gray platelet syndrome
Health Risk
RS200100160
Conflicting classifications of pathogenicity
Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
Health Risk
RS200121105
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS200204458
Conflicting classifications of pathogenicity
NBEAL2-related disorder, Inborn genetic diseases, NBEAL2-related disorder
Health Risk
RS200622688
Conflicting classifications of pathogenicity
Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
Health Risk
RS201179667
Conflicting classifications of pathogenicity
Gray platelet syndrome, Gray platelet syndrome
Health Risk
All Variants (94)
RSID Category Clinical Significance Conditions
RS140354422 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
RS144664865 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
RS145760682 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
RS181413143 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
RS185057557 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
RS187699322 Health Risk Conflicting classifications of pathogenicity
RS199797249 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS200100160 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
RS200121105 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS200204458 Health Risk Conflicting classifications of pathogenicity NBEAL2-related disorder, Inborn genetic diseases, NBEAL2-related disorder
RS200622688 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Thrombocytopenia, Abnormal bleeding
RS201179667 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS201373710 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS201641746 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
RS201749187 Health Risk Conflicting classifications of pathogenicity NBEAL2-related disorder, Inborn genetic diseases, NBEAL2-related disorder
RS202066156 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS202204936 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS367672629 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS368375664 Health Risk Conflicting classifications of pathogenicity NBEAL2-related disorder, NBEAL2-related disorder
RS369363563 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
RS369906164 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS369931526 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS370559049 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Colon adenocarcinoma
RS371065166 Health Risk Conflicting classifications of pathogenicity
RS371129706 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS371768924 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Gray platelet syndrome
RS372705263 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS374154267 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS374608720 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS375726193 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS528681375 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
RS554449998 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS557640338 Health Risk Conflicting classifications of pathogenicity NBEAL2-related disorder, NBEAL2-related disorder
RS577957158 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
RS749279630 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Gray platelet syndrome
RS771754714 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, Inborn genetic diseases, Gray platelet syndrome
RS776191203 Health Risk Conflicting classifications of pathogenicity Gray platelet syndrome, NBEAL2-related disorder, Inborn genetic diseases
RS1222222566 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1233482159 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1235183015 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1339171276 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1341020147 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1575619957 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS1575628744 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS2035871619 Health Risk Likely pathogenic
RS2037415464 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS2037417315 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS2107337553 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS2107346255 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
RS2107413869 Health Risk Likely pathogenic Gray platelet syndrome, Gray platelet syndrome
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