MPI Chromosome 15

Mannose phosphate isomerase
132 variants 132 Health Risk

Upload your DNA to see your personal genotypes for variants in MPI.

What This Gene Does
Phosphomannose isomerase catalyzes the interconversion of fructose-6-phosphate and mannose-6-phosphate and plays a critical role in maintaining the supply of D-mannose derivatives, which are required for most glycosylation reactions. Mutations in the MPI gene were found in patients with carbohydrate-deficient glycoprotein syndrome, type Ib. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2014]
Associated Conditions (2)
MPI-congenital disorder of glycosylation
MPI-related disorder
Key Variants
RS1057516550
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-related disorder, MPI-congenital disorder of glycosylation
Health Risk
RS1268293635
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS139228075
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS139866632
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS143982014
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-related disorder, MPI-congenital disorder of glycosylation
Health Risk
RS144118442
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS150217523
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS1595822583
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS199719453
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS199972529
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS200903491
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
RS2064752971
Conflicting classifications of pathogenicity
MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
Health Risk
All Variants (132)
RSID Category Clinical Significance Conditions
RS1057516550 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-related disorder, MPI-congenital disorder of glycosylation
RS1268293635 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS139228075 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS139866632 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS143982014 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-related disorder, MPI-congenital disorder of glycosylation
RS144118442 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS150217523 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1595822583 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS199719453 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS199972529 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS200903491 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064752971 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064840907 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064843052 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS377419930 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS528828174 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS564765063 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS748090636 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS752948071 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS766458792 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS768029221 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS773678732 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS778577329 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS794727716 Health Risk Conflicting classifications of pathogenicity MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS104894495 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1057516466 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1057516573 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1057517115 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1225376562 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1237538373 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1394866894 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1435343419 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555478015 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555478118 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555478333 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555478582 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555478606 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555479227 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555479341 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1555479441 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1567269757 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS1596441025 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064727120 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064828055 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2064832233 Health Risk Likely pathogenic
RS2141194911 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2141194926 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2141200280 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2141206921 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
RS2141208628 Health Risk Likely pathogenic MPI-congenital disorder of glycosylation, MPI-congenital disorder of glycosylation
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