MPDZ Chromosome 9

Multiple PDZ domain crumbs cell polarity complex component
143 variants 143 Health Risk

Upload your DNA to see your personal genotypes for variants in MPDZ.

What This Gene Does
The protein encoded by this gene has multiple PDZ domains, which are hallmarks of protein-protein interactions. The encoded protein is known to interact with the HTR2C receptor and may cause it to clump at the cell surface. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Aug 2015]
Gene Info
Gene Group
"PDZ domain containing|Crumbs complex components"
Locus Type
gene with protein product
Location
9p23
Ensembl
ENSG00000107186
Associated Conditions (6)
Inborn genetic diseases
MPDZ-related disorder
Hydrocephalus
nonsyndromic
autosomal recessive 2
Congenital hydrocephalus
Key Variants
All Variants (143)
RSID Category Clinical Significance Conditions
RS1554678324 Health Risk Likely pathogenic
RS1563840864 Health Risk Likely pathogenic
RS1586841546 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS1587783980 Health Risk Likely pathogenic
RS1942752972 Health Risk Likely pathogenic
RS1945141397 Health Risk Likely pathogenic
RS1951349487 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS1951383421 Health Risk Likely pathogenic
RS1959088978 Health Risk Likely pathogenic
RS1959174597 Health Risk Likely pathogenic
RS1959559533 Health Risk Likely pathogenic
RS2131668162 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS2133382439 Health Risk Likely pathogenic
RS2134192926 Health Risk Likely pathogenic
RS2493075833 Health Risk Likely pathogenic
RS2494469980 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS2497668341 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS2538474549 Health Risk Likely pathogenic
RS746360632 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS750355280 Health Risk Likely pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS757886671 Health Risk Likely pathogenic
RS767539728 Health Risk Likely pathogenic
RS767669471 Health Risk Likely pathogenic
RS775394111 Health Risk Likely pathogenic MPDZ-related disorder, Hydrocephalus, nonsyndromic
RS778600333 Health Risk Likely pathogenic
RS928594835 Health Risk Likely pathogenic
RS1220735820 Health Risk Pathogenic
RS1223873838 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1267168609 Health Risk Pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS1297645338 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1347266016 Health Risk Pathogenic
RS1362046514 Health Risk Pathogenic
RS1453829048 Health Risk Pathogenic
RS1490841403 Health Risk Pathogenic
RS1563886845 Health Risk Pathogenic Inborn genetic diseases, Inborn genetic diseases
RS1563948056 Health Risk Pathogenic
RS1564026963 Health Risk Pathogenic
RS1942945941 Health Risk Pathogenic
RS1947102571 Health Risk Pathogenic
RS1947104738 Health Risk Pathogenic
RS1956840371 Health Risk Pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS1958831021 Health Risk Pathogenic
RS1959180291 Health Risk Pathogenic
RS200131423 Health Risk Pathogenic
RS2131610068 Health Risk Pathogenic Hydrocephalus, nonsyndromic, autosomal recessive 2
RS2133385585 Health Risk Pathogenic
RS2489784650 Health Risk Pathogenic
RS2490783211 Health Risk Pathogenic
RS2490785037 Health Risk Pathogenic
RS2493637951 Health Risk Pathogenic
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