MCIDAS Chromosome 5

Multiciliate differentiation and DNA synthesis associated cell cycle protein
19 variants 19 Health Risk

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What This Gene Does
This gene encodes a member of the geminin family of proteins. The encoded nuclear protein is required for the generation of multiciliated cells in respiratory epithelium. Mutations in this gene cause a rare mucociliary clearance disorder associated with recurring respiratory infections in human patients, known as reduced generation of multiple motile cilia (RGMC). [provided by RefSeq, Sep 2016]
Associated Conditions (7)
Primary ciliary dyskinesia
Inborn genetic diseases
Ciliary dyskinesia
primary
42
MCIDAS-related disorder
Primary ciliary dyskinesia 3
Key Variants
All Variants (19)
RSID Category Clinical Significance Conditions
RS113717721 Health Risk Conflicting classifications of pathogenicity Primary ciliary dyskinesia, Inborn genetic diseases, Primary ciliary dyskinesia
RS181955833 Health Risk Conflicting classifications of pathogenicity Primary ciliary dyskinesia, Ciliary dyskinesia, primary
RS185737637 Health Risk Conflicting classifications of pathogenicity Primary ciliary dyskinesia, MCIDAS-related disorder, Ciliary dyskinesia
RS186341559 Health Risk Conflicting classifications of pathogenicity Primary ciliary dyskinesia, Ciliary dyskinesia, primary
RS199825346 Health Risk Conflicting classifications of pathogenicity Primary ciliary dyskinesia, Ciliary dyskinesia, primary
RS2478513634 Health Risk Likely pathogenic Ciliary dyskinesia, primary, 42
RS797045152 Health Risk Likely pathogenic Ciliary dyskinesia, primary, 42
RS939457499 Health Risk Likely pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS1478876274 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS1561117442 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS1580402818 Health Risk Pathogenic Ciliary dyskinesia, primary, 42
RS1745348853 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS1745349301 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS2111702150 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS2478513916 Health Risk Pathogenic Primary ciliary dyskinesia 3, Primary ciliary dyskinesia 3
RS2478527360 Health Risk Pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
RS777031813 Health Risk Pathogenic Ciliary dyskinesia, primary, 42
RS797045151 Health Risk Pathogenic Ciliary dyskinesia, primary, 42
RS1291689114 Health Risk Pathogenic/Likely pathogenic Primary ciliary dyskinesia, Primary ciliary dyskinesia
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