MATN3 Chromosome 2

Matrilin 3
28 variants 28 Health Risk

Upload your DNA to see your personal genotypes for variants in MATN3.

What This Gene Does
This gene encodes a member of von Willebrand factor A domain containing protein family. This family of proteins is thought to be involved in the formation of filamentous networks in the extracellular matrices of various tissues. This protein contains two von Willebrand factor A domains; it is present in the cartilage extracellular matrix and has a role in the development and homeostasis of cartilage and bone. Mutations in this gene result in multiple epiphyseal dysplasia. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
Matrilins
Locus Type
gene with protein product
Location
2p24.1
Ensembl
ENSG00000132031
Associated Conditions (8)
Inborn genetic diseases
Multiple epiphyseal dysplasia type 5
Connective tissue disorder
MATN3-related disorder
Multiple epiphyseal dysplasia
Osteoarthritis susceptibility 2
Spondyloepimetaphyseal dysplasia
matrilin-3 type
Key Variants
RS138400723
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS1401043626
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
RS1422262650
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
RS1673092558
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
RS182164052
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
RS201458413
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS201563567
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
RS201755444
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Connective tissue disorder, MATN3-related disorder
Health Risk
RS563628955
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Inborn genetic diseases, Multiple epiphyseal dysplasia type 5
Health Risk
RS571353547
Conflicting classifications of pathogenicity
Connective tissue disorder, Connective tissue disorder
Health Risk
RS573907581
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Inborn genetic diseases, Multiple epiphyseal dysplasia type 5
Health Risk
RS745766346
Conflicting classifications of pathogenicity
Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
Health Risk
All Variants (28)
RSID Category Clinical Significance Conditions
RS138400723 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1401043626 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS1422262650 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS1673092558 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS182164052 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS201458413 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS201563567 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS201755444 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Connective tissue disorder, MATN3-related disorder
RS563628955 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Inborn genetic diseases, Multiple epiphyseal dysplasia type 5
RS571353547 Health Risk Conflicting classifications of pathogenicity Connective tissue disorder, Connective tissue disorder
RS573907581 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Inborn genetic diseases, Multiple epiphyseal dysplasia type 5
RS745766346 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS753889985 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS760753512 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS773883750 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS774204299 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Inborn genetic diseases, Multiple epiphyseal dysplasia type 5
RS886043710 Health Risk Conflicting classifications of pathogenicity
RS993108436 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS996766896 Health Risk Conflicting classifications of pathogenicity Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS1673102663 Health Risk Likely pathogenic Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS2103484088 Health Risk Likely pathogenic Multiple epiphyseal dysplasia, Multiple epiphyseal dysplasia
RS749515743 Health Risk Likely pathogenic Osteoarthritis susceptibility 2, Osteoarthritis susceptibility 2
RS104893639 Health Risk Pathogenic Spondyloepimetaphyseal dysplasia, matrilin-3 type, Spondyloepimetaphyseal dysplasia
RS104893641 Health Risk Pathogenic Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia type 5
RS104893645 Health Risk Pathogenic Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia, Multiple epiphyseal dysplasia type 5
RS28939677 Health Risk Pathogenic Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia, Multiple epiphyseal dysplasia type 5
RS104893637 Health Risk Pathogenic/Likely pathogenic Multiple epiphyseal dysplasia type 5, Multiple epiphyseal dysplasia, Spondyloepimetaphyseal dysplasia
RS397515546 Health Risk Pathogenic/Likely pathogenic Multiple epiphyseal dysplasia type 5, Spondyloepimetaphyseal dysplasia, matrilin-3 type
Sign Up to Analyze Your DNA Log In