MAK Chromosome 6

Male germ cell associated kinase
106 variants 106 Health Risk

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What This Gene Does
The product of this gene is a serine/threonine protein kinase related to kinases involved in cell cycle regulation. Studies of the mouse and rat homologs have localized the kinase to the chromosomes during meiosis in spermatogenesis, specifically to the synaptonemal complex that exists while homologous chromosomes are paired. Mutations in this gene have been associated with ciliary defects resulting in retinitis pigmentosa 62. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016]
Gene Info
Gene Group
CILK1, MAK, MOK protein kinase family
Locus Type
gene with protein product
Location
6p24.2
Ensembl
ENSG00000111837
Associated Conditions (9)
Inborn genetic diseases
Retinitis pigmentosa 62
Retinal dystrophy
Retinitis pigmentosa
MAK-related disorder
Familial pancreatic carcinoma
Malignant tumor of esophagus
MAK-related retinopathy
Isolated macular dystrophy
Key Variants
All Variants (106)
RSID Category Clinical Significance Conditions
RS139003494 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1394158081 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS144848825 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS145014649 Health Risk Conflicting classifications of pathogenicity
RS1459871246 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS147251038 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS149006687 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1772880607 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS1775529306 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS199594233 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS200641218 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Inborn genetic diseases, Retinal dystrophy
RS200703968 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS201628941 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS202001756 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, MAK-related disorder, Retinitis pigmentosa
RS375070639 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS387906647 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa 62, Retinal dystrophy, Retinitis pigmentosa 62
RS527236080 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa
RS540144059 Health Risk Conflicting classifications of pathogenicity
RS56217305 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS756170824 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS764870230 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS767830843 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Inborn genetic diseases, Retinal dystrophy
RS76972797 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Familial pancreatic carcinoma, Malignant tumor of esophagus
RS774229391 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinitis pigmentosa, Retinal dystrophy
RS776541315 Health Risk Conflicting classifications of pathogenicity Retinitis pigmentosa, Retinitis pigmentosa
RS868081622 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS990185904 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1201940872 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1300819259 Health Risk Likely pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1450447701 Health Risk Likely pathogenic MAK-related retinopathy, MAK-related retinopathy
RS1453700499 Health Risk Likely pathogenic
RS1581697849 Health Risk Likely pathogenic Retinitis pigmentosa, Retinitis pigmentosa
RS1776708773 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS1776708973 Health Risk Likely pathogenic Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS1778747154 Health Risk Likely pathogenic
RS2127548040 Health Risk Likely pathogenic Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS2127556087 Health Risk Likely pathogenic
RS2532398657 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS2532653369 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS387906646 Health Risk Likely pathogenic Retinitis pigmentosa 62, Retinal dystrophy, Retinitis pigmentosa 62
RS749769834 Health Risk Likely pathogenic
RS759932426 Health Risk Likely pathogenic
RS766527083 Health Risk Likely pathogenic
RS780978066 Health Risk Likely pathogenic Retinitis pigmentosa 62, Retinitis pigmentosa 62
RS1037177330 Health Risk Pathogenic
RS1274912017 Health Risk Pathogenic
RS1288620533 Health Risk Pathogenic
RS1320050201 Health Risk Pathogenic
RS1341598207 Health Risk Pathogenic
RS1382310091 Health Risk Pathogenic
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