LRRC56 Chromosome 11

Leucine rich repeat containing 56
23 variants 23 Health Risk

Upload your DNA to see your personal genotypes for variants in LRRC56.

What This Gene Does
Predicted to be involved in cell projection organization. Predicted to be located in cilium. Implicated in primary ciliary dyskinesia 39. [provided by Alliance of Genome Resources, Jul 2025]
Gene Info
Gene Group
Axonemal dynein assembly factors
Locus Type
gene with protein product
Location
11p15.5
Ensembl
ENSG00000161328
Associated Conditions (5)
LRRC56-related disorder
Ciliary dyskinesia
primary
39
Kartagener syndrome
Key Variants
All Variants (23)
RSID Category Clinical Significance Conditions
RS113808353 Health Risk Conflicting classifications of pathogenicity
RS138766042 Health Risk Conflicting classifications of pathogenicity LRRC56-related disorder, LRRC56-related disorder
RS149919024 Health Risk Conflicting classifications of pathogenicity Ciliary dyskinesia, primary, 39
RS1852307190 Health Risk Conflicting classifications of pathogenicity Ciliary dyskinesia, primary, 39
RS372006680 Health Risk Conflicting classifications of pathogenicity
RS752363538 Health Risk Conflicting classifications of pathogenicity
RS752922900 Health Risk Conflicting classifications of pathogenicity LRRC56-related disorder, LRRC56-related disorder
RS772525350 Health Risk Conflicting classifications of pathogenicity
RS1331420078 Health Risk Likely pathogenic
RS2539909801 Health Risk Likely pathogenic
RS2539928316 Health Risk Likely pathogenic
RS1221197180 Health Risk Pathogenic
RS138918564 Health Risk Pathogenic LRRC56-related disorder, LRRC56-related disorder
RS1564800859 Health Risk Pathogenic Ciliary dyskinesia, primary, 39
RS1564805039 Health Risk Pathogenic Ciliary dyskinesia, primary, 39
RS1564805053 Health Risk Pathogenic Ciliary dyskinesia, primary, 39
RS2539921362 Health Risk Pathogenic
RS2539932445 Health Risk Pathogenic
RS2539933089 Health Risk Pathogenic
RS372959912 Health Risk Pathogenic Ciliary dyskinesia, primary, 39
RS761092893 Health Risk Pathogenic
RS1421592107 Health Risk Pathogenic/Likely pathogenic Kartagener syndrome, Kartagener syndrome
RS2539848777 Health Risk Pathogenic/Likely pathogenic Ciliary dyskinesia, primary, 39
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