LMNB1 Chromosome 5

Lamin B1
23 variants 23 Health Risk

Upload your DNA to see your personal genotypes for variants in LMNB1.

What This Gene Does
This gene encodes one of the two B-type lamin proteins and is a component of the nuclear lamina. A duplication of this gene is associated with autosomal dominant adult-onset leukodystrophy (ADLD). Alternative splicing results in multiple transcript variants. [provided by RefSeq, Dec 2015]
Gene Info
Gene Group
Lamins
Locus Type
gene with protein product
Location
5q23.2
Ensembl
ENSG00000113368
Associated Conditions (8)
Inborn genetic diseases
Adult-onset autosomal dominant demyelinating leukodystrophy
Cervical cancer
Microcephaly 26
primary
autosomal dominant
Syndrome with microcephaly as major feature
Microcephaly
Key Variants
RS1187296225
Conflicting classifications of pathogenicity
Health Risk
RS138778484
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS142016804
Conflicting classifications of pathogenicity
Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
Health Risk
RS150504258
Conflicting classifications of pathogenicity
Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
Health Risk
RS190794874
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS368286117
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS370551700
Conflicting classifications of pathogenicity
Adult-onset autosomal dominant demyelinating leukodystrophy, Cervical cancer, Adult-onset autosomal dominant demyelinating leukodystrophy
Health Risk
RS370881377
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS372984423
Conflicting classifications of pathogenicity
Health Risk
RS374998378
Conflicting classifications of pathogenicity
Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
Health Risk
RS546757986
Conflicting classifications of pathogenicity
Inborn genetic diseases, Inborn genetic diseases
Health Risk
RS550205958
Conflicting classifications of pathogenicity
Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
Health Risk
All Variants (23)
RSID Category Clinical Significance Conditions
RS1187296225 Health Risk Conflicting classifications of pathogenicity
RS138778484 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS142016804 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
RS150504258 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
RS190794874 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS368286117 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS370551700 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Cervical cancer, Adult-onset autosomal dominant demyelinating leukodystrophy
RS370881377 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS372984423 Health Risk Conflicting classifications of pathogenicity
RS374998378 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
RS546757986 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS550205958 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
RS746416284 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Adult-onset autosomal dominant demyelinating leukodystrophy
RS757576125 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Microcephaly 26, primary
RS758245272 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS771251880 Health Risk Conflicting classifications of pathogenicity Adult-onset autosomal dominant demyelinating leukodystrophy, Inborn genetic diseases, Adult-onset autosomal dominant demyelinating leukodystrophy
RS1750506249 Health Risk Likely pathogenic Microcephaly 26, primary, autosomal dominant
RS2479520123 Health Risk Likely pathogenic Microcephaly 26, primary, autosomal dominant
RS1245844735 Health Risk Pathogenic Syndrome with microcephaly as major feature, Microcephaly 26, primary
RS1750497172 Health Risk Pathogenic Syndrome with microcephaly as major feature, Microcephaly 26, primary
RS1751587092 Health Risk Pathogenic Microcephaly 26, primary, autosomal dominant
RS1751797979 Health Risk Pathogenic Microcephaly, Microcephaly
RS935132421 Health Risk Pathogenic Microcephaly 26, primary, autosomal dominant
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