LIM2 Chromosome 19

Lens intrinsic membrane protein 2
9 variants 9 Health Risk

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What This Gene Does
This gene encodes an eye lens-specific protein found at the junctions of lens fiber cells, where it may contribute to cell junctional organization. It acts as a receptor for calmodulin, and may play an important role in both lens development and cataractogenesis. Mutations in this gene have been associated with cataract formation. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Sep 2009]
Associated Conditions (4)
Cataract 19 multiple types
LIM2-related disorder
Inborn genetic diseases
Cataract
Key Variants
All Variants (9)
RSID Category Clinical Significance Conditions
RS142517355 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, LIM2-related disorder, Inborn genetic diseases
RS145192236 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, Cataract 19 multiple types
RS147625714 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, Cataract 19 multiple types
RS574581011 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, Inborn genetic diseases, Cataract 19 multiple types
RS73934370 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, Cataract 19 multiple types, Inborn genetic diseases
RS8111243 Health Risk Conflicting classifications of pathogenicity Cataract 19 multiple types, Cataract 19 multiple types
RS121913555 Health Risk Pathogenic Cataract 19 multiple types, Cataract 19 multiple types
RS869312732 Health Risk Pathogenic Cataract 19 multiple types, Cataract 19 multiple types
RS1568480054 Health Risk Pathogenic/Likely pathogenic Cataract, Cataract 19 multiple types, LIM2-related disorder
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