LDLRAP1 Chromosome 1

Low density lipoprotein receptor adaptor protein 1
85 variants 85 Health Risk

Upload your DNA to see your personal genotypes for variants in LDLRAP1.

What This Gene Does
The protein encoded by this gene is a cytosolic protein which contains a phosphotyrosine binding (PTD) domain. The PTD domain has been found to interact with the cytoplasmic tail of the LDL receptor. Mutations in this gene lead to LDL receptor malfunction and cause the disorder autosomal recessive hypercholesterolaemia. [provided by RefSeq, Jul 2008]
Associated Conditions (8)
Hypercholesterolemia
familial
4
Familial hypercholesterolemia
Cardiovascular phenotype
LDLRAP1-related disorder
Autosomal recessive inheritance
See cases
Key Variants
All Variants (85)
RSID Category Clinical Significance Conditions
RS1057515462 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS1057515463 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS1057515534 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS1057515536 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS114583297 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS1215026981 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS121908326 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS139877665 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS140170877 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS141522360 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS142920998 Health Risk Conflicting classifications of pathogenicity Familial hypercholesterolemia, Hypercholesterolemia, familial
RS143563728 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Hypercholesterolemia, familial
RS144622500 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS146122441 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS146134293 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS199605881 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS201198223 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS202247605 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS2043860268 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS369497122 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS371561646 Health Risk Conflicting classifications of pathogenicity Familial hypercholesterolemia, Hypercholesterolemia, familial
RS372215069 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS375900985 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS386629678 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS41291054 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS41291058 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS563151154 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS568643238 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS575024313 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS747011377 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS753806649 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, Cardiovascular phenotype
RS763971300 Health Risk Conflicting classifications of pathogenicity Cardiovascular phenotype, LDLRAP1-related disorder, Hypercholesterolemia
RS767432973 Health Risk Conflicting classifications of pathogenicity Hypercholesterolemia, familial, 4
RS1019504966 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS1252720524 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS1294326404 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS1461905374 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS1572052376 Health Risk Likely pathogenic
RS2044161691 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS2124667505 Health Risk Likely pathogenic
RS2523992082 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS2524003925 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS2524136302 Health Risk Likely pathogenic Cardiovascular phenotype, Cardiovascular phenotype
RS762148512 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS769595182 Health Risk Likely pathogenic Hypercholesterolemia, familial, 4
RS1057515537 Health Risk Pathogenic Hypercholesterolemia, familial, 4
RS121908324 Health Risk Pathogenic Hypercholesterolemia, familial, 4
RS121908325 Health Risk Pathogenic Hypercholesterolemia, familial, 4
RS1330017675 Health Risk Pathogenic Hypercholesterolemia, familial, 4
RS1430518299 Health Risk Pathogenic Hypercholesterolemia, familial, 4
Sign Up to Analyze Your DNA Log In