KRAS Chromosome 12

KRAS proto-oncogene, GTPase
81 variants 81 Health Risk

Upload your DNA to see your personal genotypes for variants in KRAS.

What This Gene Does
This gene, a Kirsten ras oncogene homolog from the mammalian ras gene family, encodes a protein that is a member of the small GTPase superfamily. A single amino acid substitution is responsible for an activating mutation. The transforming protein that results is implicated in various malignancies, including lung adenocarcinoma, mucinous adenoma, ductal carcinoma of the pancreas and colorectal carcinoma. Alternative splicing leads to variants encoding two isoforms that differ in the C-terminal region. [provided by RefSeq, Jul 2008]
Gene Info
Gene Group
RAS type GTPase family
Locus Type
gene with protein product
Location
12p12.1
Ensembl
ENSG00000133703
Associated Conditions (89)
Noonan syndrome
RASopathy
12 conditions
Noonan syndrome 3
Non-small cell lung carcinoma
Cerebral arteriovenous malformation
Vascular malformation
Juvenile myelomonocytic leukemia
Cardiovascular phenotype
Primary intracranial sarcoma
DICER1-mutant
Colorectal cancer
Neoplasm
Pilocytic astrocytoma
Embryonal rhabdomyosarcoma
Carcinoma of pancreas
KRAS-related disorder
Cardio-facio-cutaneous syndrome
Acute myeloid leukemia
Cardiofaciocutaneous syndrome 2
+69 more conditions
Key Variants
All Variants (81)
RSID Category Clinical Significance Conditions
RS104894361 Health Risk Pathogenic Cardiofaciocutaneous syndrome 2, Inborn genetic diseases, RASopathy
RS104894362 Health Risk Pathogenic Cardiofaciocutaneous syndrome 2, RASopathy, KRAS-related disorder
RS104894364 Health Risk Pathogenic Noonan syndrome 3, Noonan syndrome, RASopathy
RS104894365 Health Risk Pathogenic Noonan syndrome 3, Endometrial carcinoma, RASopathy
RS104894367 Health Risk Pathogenic Noonan syndrome 3, Noonan syndrome 3
RS1064796748 Health Risk Pathogenic
RS112445441 Health Risk Pathogenic Breast adenocarcinoma, Non-small cell lung carcinoma, Juvenile myelomonocytic leukemia
RS121913238 Health Risk Pathogenic Non-small cell lung carcinoma, Colon adenocarcinoma, Thyroid cancer
RS121913240 Health Risk Pathogenic Noonan syndrome, RASopathy, Noonan syndrome and Noonan-related syndrome
RS121913530 Health Risk Pathogenic Lung carcinoma, Non-small cell lung carcinoma, Endometrial carcinoma
RS1565878932 Health Risk Pathogenic
RS2135806030 Health Risk Pathogenic Noonan syndrome 3, Noonan syndrome 3
RS2135806200 Health Risk Pathogenic
RS2135806256 Health Risk Pathogenic
RS2141506264 Health Risk Pathogenic
RS2141509932 Health Risk Pathogenic Capillary Telangiectasia, Brain, Capillary Telangiectasia
RS2141509973 Health Risk Pathogenic Noonan syndrome 3, Noonan syndrome 3
RS2548909825 Health Risk Pathogenic RASopathy, RASopathy
RS397517042 Health Risk Pathogenic Noonan syndrome, Noonan syndrome, Cardio-facio-cutaneous syndrome
RS606231202 Health Risk Pathogenic Acute myeloid leukemia, Acute myeloid leukemia
RS727504662 Health Risk Pathogenic Noonan syndrome, RASopathy, RASopathy
RS770248150 Health Risk Pathogenic Encephalocraniocutaneous lipomatosis, Colorectal cancer, Primary intracranial sarcoma
RS104894360 Health Risk Pathogenic/Likely pathogenic Cardiofaciocutaneous syndrome 2, Noonan syndrome 3, RASopathy
RS1057519725 Health Risk Pathogenic/Likely pathogenic OCULOECTODERMAL SYNDROME, SOMATIC, Encephalocraniocutaneous lipomatosis
RS121913236 Health Risk Pathogenic/Likely pathogenic RASopathy, Linear nevus sebaceous syndrome, RASopathy
RS121913527 Health Risk Pathogenic/Likely pathogenic RASopathy, OCULOECTODERMAL SYNDROME, SOMATIC
RS121913528 Health Risk Pathogenic/Likely pathogenic Bladder cancer, transitional cell, somatic
RS121913529 Health Risk Pathogenic/Likely pathogenic Carcinoma of pancreas, Epidermal nevus, Nevus sebaceous
RS121913535 Health Risk Pathogenic/Likely pathogenic Pilocytic astrocytoma, Non-small cell lung carcinoma, Non-small cell lung carcinoma
RS387907206 Health Risk Pathogenic/Likely pathogenic Cardiofaciocutaneous syndrome 2, Cardiofaciocutaneous syndrome 2
RS727503109 Health Risk Pathogenic/Likely pathogenic RASopathy, Cardio-facio-cutaneous syndrome, Noonan syndrome
Sign Up to Analyze Your DNA Log In