KIZ Chromosome 20

Kizuna centrosomal protein
54 variants 54 Health Risk

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What This Gene Does
The protein encoded by this gene localizes to centrosomes, strengthening and stabilizing the pericentriolar region prior to spindle formation. The encoded protein usually remains with the mother centrosome after centrosomal duplication. Sevral transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Feb 2013]
Associated Conditions (13)
Retinal dystrophy
Papillary renal cell carcinoma type 1
Retinitis pigmentosa 69
Lung cancer
Adrenocortical carcinoma
hereditary
Retinitis pigmentosa
KIZ-related disorder
Neurodevelopmental disorder
mitochondrial
with abnormal movements and lactic acidosis
with or without seizures
KIZ-related retinopathy
Key Variants
All Variants (54)
RSID Category Clinical Significance Conditions
RS11087346 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS1477553904 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS201376938 Health Risk Conflicting classifications of pathogenicity
RS370051792 Health Risk Conflicting classifications of pathogenicity
RS372338345 Health Risk Conflicting classifications of pathogenicity
RS373803095 Health Risk Conflicting classifications of pathogenicity
RS755436546 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS756423093 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS758224894 Health Risk Conflicting classifications of pathogenicity Retinal dystrophy, Retinal dystrophy
RS758692347 Health Risk Conflicting classifications of pathogenicity
RS760383931 Health Risk Conflicting classifications of pathogenicity
RS1190041303 Health Risk Likely pathogenic
RS1205920781 Health Risk Likely pathogenic
RS1270017793 Health Risk Likely pathogenic
RS1358557669 Health Risk Likely pathogenic
RS2122310534 Health Risk Likely pathogenic Retinal dystrophy, Retinal dystrophy
RS2514836751 Health Risk Likely pathogenic
RS748951603 Health Risk Likely pathogenic Papillary renal cell carcinoma type 1, Papillary renal cell carcinoma type 1
RS750369135 Health Risk Likely pathogenic Retinitis pigmentosa 69, Retinitis pigmentosa 69
RS750460795 Health Risk Likely pathogenic Lung cancer, Lung cancer
RS754547088 Health Risk Likely pathogenic Adrenocortical carcinoma, hereditary, Adrenocortical carcinoma
RS1353241230 Health Risk Pathogenic
RS1429038413 Health Risk Pathogenic
RS1439979978 Health Risk Pathogenic
RS1457725246 Health Risk Pathogenic
RS199700362 Health Risk Pathogenic
RS202210819 Health Risk Pathogenic Retinitis pigmentosa 69, Retinal dystrophy, Retinitis pigmentosa
RS2031451980 Health Risk Pathogenic Retinitis pigmentosa 69, Retinitis pigmentosa 69
RS2032191781 Health Risk Pathogenic
RS2032195039 Health Risk Pathogenic
RS2122229308 Health Risk Pathogenic
RS2122691390 Health Risk Pathogenic
RS2123451202 Health Risk Pathogenic
RS2519757098 Health Risk Pathogenic
RS587777377 Health Risk Pathogenic Retinitis pigmentosa 69, Retinal dystrophy, Retinitis pigmentosa
RS747573633 Health Risk Pathogenic
RS749011772 Health Risk Pathogenic
RS754100363 Health Risk Pathogenic
RS755731853 Health Risk Pathogenic
RS760768357 Health Risk Pathogenic
RS762733814 Health Risk Pathogenic
RS766568333 Health Risk Pathogenic Retinitis pigmentosa 69, Retinitis pigmentosa 69
RS769530569 Health Risk Pathogenic
RS770989376 Health Risk Pathogenic
RS988408197 Health Risk Pathogenic
RS1254494198 Health Risk Pathogenic/Likely pathogenic Retinitis pigmentosa, Retinal dystrophy, Retinitis pigmentosa
RS1282376513 Health Risk Pathogenic/Likely pathogenic Retinal dystrophy, Retinitis pigmentosa 69, Retinal dystrophy
RS1438134533 Health Risk Pathogenic/Likely pathogenic
RS1444145965 Health Risk Pathogenic/Likely pathogenic Retinitis pigmentosa 69, Retinitis pigmentosa 69
RS1486270427 Health Risk Pathogenic/Likely pathogenic Neurodevelopmental disorder, mitochondrial, with abnormal movements and lactic acidosis
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