KCNC3 Chromosome 19

Potassium voltage-gated channel subfamily C member 3
25 variants 25 Health Risk

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What This Gene Does
The Shaker gene family of Drosophila encodes components of voltage-gated potassium channels and is comprised of four subfamilies. Based on sequence similarity, this gene is similar to one of these subfamilies, namely the Shaw subfamily. The protein encoded by this gene belongs to the delayed rectifier class of channel proteins and is an integral membrane protein that mediates the voltage-dependent potassium ion permeability of excitable membranes. Alternate splicing results in several transcript variants. [provided by RefSeq, Mar 2014]
Gene Info
Gene Group
"Potassium voltage-gated channels|BTB domain containing"
Locus Type
gene with protein product
Location
19q13.33
Ensembl
ENSG00000131398
Associated Conditions (6)
Inborn genetic diseases
Spinocerebellar ataxia type 13
Tip-toe gait
KCNC3-related disorder
Cleft palate
Hereditary ataxia
Key Variants
All Variants (25)
RSID Category Clinical Significance Conditions
RS1034583217 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1057519247 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1326942763 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Spinocerebellar ataxia type 13, Inborn genetic diseases
RS148033381 Health Risk Conflicting classifications of pathogenicity
RS199833067 Health Risk Conflicting classifications of pathogenicity
RS368232448 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Spinocerebellar ataxia type 13, Inborn genetic diseases
RS375782591 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS558106649 Health Risk Conflicting classifications of pathogenicity
RS568711737 Health Risk Conflicting classifications of pathogenicity
RS747618525 Health Risk Conflicting classifications of pathogenicity Spinocerebellar ataxia type 13, Tip-toe gait, Spinocerebellar ataxia type 13
RS761806977 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, KCNC3-related disorder, Inborn genetic diseases
RS764571894 Health Risk Conflicting classifications of pathogenicity Spinocerebellar ataxia type 13, Inborn genetic diseases, Cleft palate
RS770686560 Health Risk Conflicting classifications of pathogenicity Spinocerebellar ataxia type 13, Spinocerebellar ataxia type 13
RS927538730 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS969993818 Health Risk Conflicting classifications of pathogenicity Inborn genetic diseases, Inborn genetic diseases
RS1064795793 Health Risk Likely pathogenic
RS1408825410 Health Risk Likely pathogenic
RS2037067131 Health Risk Likely pathogenic Spinocerebellar ataxia type 13, Spinocerebellar ataxia type 13
RS2513799489 Health Risk Likely pathogenic
RS371116909 Health Risk Likely pathogenic Tip-toe gait, Tip-toe gait
RS104894699 Health Risk Pathogenic Spinocerebellar ataxia type 13, Hereditary ataxia, Spinocerebellar ataxia type 13
RS104894700 Health Risk Pathogenic Spinocerebellar ataxia type 13, Spinocerebellar ataxia type 13
RS1555781806 Health Risk Pathogenic Spinocerebellar ataxia type 13, Spinocerebellar ataxia type 13
RS797044872 Health Risk Pathogenic Inborn genetic diseases, Spinocerebellar ataxia type 13, Inborn genetic diseases
RS879253883 Health Risk Pathogenic Spinocerebellar ataxia type 13, Spinocerebellar ataxia type 13
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